Isolated persistent left-sided superior vena cava, giant coronary sinus, atrial tachycardia and heart failure in a child

• Main Authors: Nagaraja Moorthy, Aditya Kapoor, Sudeep Kumar
• Format: Article
• Language: English
• Published: Elsevier 2013-09-01
• Series: Indian Heart Journal
• Subjects: Atrial tachycardia; Congestive heart failure; Coronary sinus; Persistent LSVC
• Online Access: http://www.sciencedirect.com/science/article/pii/S001948321300254X

Persistence of a left-sided superior vena cava (PLSVC) with absent right superior vena cava (isolated PLSVC) is a very rare venous malformation and commonly associated with congenital heart disease or alterations of the cardiac situs. We describe an unusual case of a young boy presenting with persistent atrial tachycardia and congestive heart failure. He was detected to have unexplained grossly dilated right atrium, right ventricle with systolic dysfunction and a giant coronary sinus (CS). The dilated CS closely mimicked a pseudo cor-triatriatum on echocardiography. Contrast echocardiography from both arms revealed opacification of the CS before the right atrium. Bilateral upper limb venography confirmed the presence of absent right SVC and isolated persistent left SVC draining into the giant coronary sinus.