Large aortic aneurysm and dissection in a patient with Marfan's syndrome

Marfan’s syndrome is an autosomal dominant disorder of connective tissue affecting approximately1 in5000 people. In individuals with this syndrome, more than 90% of deaths from known causes result from cardiovascular complications, such as aortic dissection, aortic regurgitation, and congestive card...

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Main Authors: Fernando Pivatto Júnior, Leila Denise Cardoso Ramos, Murilo Foppa, Felipe Soares Torres
Format: Article
Language:English
Published: Hospital de Clinicas de Porto Alegre ; Universidade Federal do Rio Grande do Sul (UFRGS) 2015-04-01
Series:Clinical and Biomedical Research
Subjects:
Online Access:http://seer.ufrgs.br/index.php/hcpa/article/view/52524
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spelling doaj-0dfc92b1532145209fb6c47e795d7d782020-11-25T02:26:37ZengHospital de Clinicas de Porto Alegre ; Universidade Federal do Rio Grande do Sul (UFRGS)Clinical and Biomedical Research0101-55752357-97302015-04-0135227226Large aortic aneurysm and dissection in a patient with Marfan's syndromeFernando Pivatto Júnior0Leila Denise Cardoso Ramos1Murilo Foppa2Felipe Soares Torres3Cardiology Division, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS - Brazil Mailing address: Fernando Pivatto Júnior, MD Cardiology Division – Hospital de Clínicas de Porto Alegre Rua Ramiro Barcelos, 2350 Sala 2060 90035-903 – Porto Alegre, RS - Brazil E-mail: fpivatto@gmail.com Phone: +55 51 3359-8342Cardiology Division, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS - BrazilCardiology Division, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS - BrazilRadiology Department, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS - BrazilMarfan’s syndrome is an autosomal dominant disorder of connective tissue affecting approximately1 in5000 people. In individuals with this syndrome, more than 90% of deaths from known causes result from cardiovascular complications, such as aortic dissection, aortic regurgitation, and congestive cardiac failure. In this report, we present a patient with a large symptomatic aortic aneurysm and chronic dissection, severe aortic regurgitation and cardiomegaly, treated successfully with resection of the proximal aorta and placement of a mechanic aortic valved graft.http://seer.ufrgs.br/index.php/hcpa/article/view/52524Marfan’s syndromeaortic aneurysmdissection
collection DOAJ
language English
format Article
sources DOAJ
author Fernando Pivatto Júnior
Leila Denise Cardoso Ramos
Murilo Foppa
Felipe Soares Torres
spellingShingle Fernando Pivatto Júnior
Leila Denise Cardoso Ramos
Murilo Foppa
Felipe Soares Torres
Large aortic aneurysm and dissection in a patient with Marfan's syndrome
Clinical and Biomedical Research
Marfan’s syndrome
aortic aneurysm
dissection
author_facet Fernando Pivatto Júnior
Leila Denise Cardoso Ramos
Murilo Foppa
Felipe Soares Torres
author_sort Fernando Pivatto Júnior
title Large aortic aneurysm and dissection in a patient with Marfan's syndrome
title_short Large aortic aneurysm and dissection in a patient with Marfan's syndrome
title_full Large aortic aneurysm and dissection in a patient with Marfan's syndrome
title_fullStr Large aortic aneurysm and dissection in a patient with Marfan's syndrome
title_full_unstemmed Large aortic aneurysm and dissection in a patient with Marfan's syndrome
title_sort large aortic aneurysm and dissection in a patient with marfan's syndrome
publisher Hospital de Clinicas de Porto Alegre ; Universidade Federal do Rio Grande do Sul (UFRGS)
series Clinical and Biomedical Research
issn 0101-5575
2357-9730
publishDate 2015-04-01
description Marfan’s syndrome is an autosomal dominant disorder of connective tissue affecting approximately1 in5000 people. In individuals with this syndrome, more than 90% of deaths from known causes result from cardiovascular complications, such as aortic dissection, aortic regurgitation, and congestive cardiac failure. In this report, we present a patient with a large symptomatic aortic aneurysm and chronic dissection, severe aortic regurgitation and cardiomegaly, treated successfully with resection of the proximal aorta and placement of a mechanic aortic valved graft.
topic Marfan’s syndrome
aortic aneurysm
dissection
url http://seer.ufrgs.br/index.php/hcpa/article/view/52524
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AT leiladenisecardosoramos largeaorticaneurysmanddissectioninapatientwithmarfanssyndrome
AT murilofoppa largeaorticaneurysmanddissectioninapatientwithmarfanssyndrome
AT felipesoarestorres largeaorticaneurysmanddissectioninapatientwithmarfanssyndrome
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