Large aortic aneurysm and dissection in a patient with Marfan's syndrome
Marfan’s syndrome is an autosomal dominant disorder of connective tissue affecting approximately1 in5000 people. In individuals with this syndrome, more than 90% of deaths from known causes result from cardiovascular complications, such as aortic dissection, aortic regurgitation, and congestive card...
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doaj-0dfc92b1532145209fb6c47e795d7d782020-11-25T02:26:37ZengHospital de Clinicas de Porto Alegre ; Universidade Federal do Rio Grande do Sul (UFRGS)Clinical and Biomedical Research0101-55752357-97302015-04-0135227226Large aortic aneurysm and dissection in a patient with Marfan's syndromeFernando Pivatto Júnior0Leila Denise Cardoso Ramos1Murilo Foppa2Felipe Soares Torres3Cardiology Division, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS - Brazil Mailing address: Fernando Pivatto Júnior, MD Cardiology Division – Hospital de Clínicas de Porto Alegre Rua Ramiro Barcelos, 2350 Sala 2060 90035-903 – Porto Alegre, RS - Brazil E-mail: fpivatto@gmail.com Phone: +55 51 3359-8342Cardiology Division, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS - BrazilCardiology Division, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS - BrazilRadiology Department, Hospital de Clínicas de Porto Alegre, Porto Alegre, RS - BrazilMarfan’s syndrome is an autosomal dominant disorder of connective tissue affecting approximately1 in5000 people. In individuals with this syndrome, more than 90% of deaths from known causes result from cardiovascular complications, such as aortic dissection, aortic regurgitation, and congestive cardiac failure. In this report, we present a patient with a large symptomatic aortic aneurysm and chronic dissection, severe aortic regurgitation and cardiomegaly, treated successfully with resection of the proximal aorta and placement of a mechanic aortic valved graft.http://seer.ufrgs.br/index.php/hcpa/article/view/52524Marfan’s syndromeaortic aneurysmdissection |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Fernando Pivatto Júnior Leila Denise Cardoso Ramos Murilo Foppa Felipe Soares Torres |
spellingShingle |
Fernando Pivatto Júnior Leila Denise Cardoso Ramos Murilo Foppa Felipe Soares Torres Large aortic aneurysm and dissection in a patient with Marfan's syndrome Clinical and Biomedical Research Marfan’s syndrome aortic aneurysm dissection |
author_facet |
Fernando Pivatto Júnior Leila Denise Cardoso Ramos Murilo Foppa Felipe Soares Torres |
author_sort |
Fernando Pivatto Júnior |
title |
Large aortic aneurysm and dissection in a patient with Marfan's syndrome |
title_short |
Large aortic aneurysm and dissection in a patient with Marfan's syndrome |
title_full |
Large aortic aneurysm and dissection in a patient with Marfan's syndrome |
title_fullStr |
Large aortic aneurysm and dissection in a patient with Marfan's syndrome |
title_full_unstemmed |
Large aortic aneurysm and dissection in a patient with Marfan's syndrome |
title_sort |
large aortic aneurysm and dissection in a patient with marfan's syndrome |
publisher |
Hospital de Clinicas de Porto Alegre ; Universidade Federal do Rio Grande do Sul (UFRGS) |
series |
Clinical and Biomedical Research |
issn |
0101-5575 2357-9730 |
publishDate |
2015-04-01 |
description |
Marfan’s syndrome is an autosomal dominant disorder of connective tissue affecting approximately1 in5000 people. In individuals with this syndrome, more than 90% of deaths from known causes result from cardiovascular complications, such as aortic dissection, aortic regurgitation, and congestive cardiac failure. In this report, we present a patient with a large symptomatic aortic aneurysm and chronic dissection, severe aortic regurgitation and cardiomegaly, treated successfully with resection of the proximal aorta and placement of a mechanic aortic valved graft. |
topic |
Marfan’s syndrome aortic aneurysm dissection |
url |
http://seer.ufrgs.br/index.php/hcpa/article/view/52524 |
work_keys_str_mv |
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