ENUCLEATION IN A PATIENT WITH NEUROFIBROMATOSIS TYPE 1 WITH BUPHTHALMOS AND OCULAR DEFORMITY

ENUCLEATION IN A PATIENT WITH NEUROFIBROMATOSIS TYPE 1 WITH BUPHTHALMOS AND OCULAR DEFORMITY

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To report a case of buphthalmos with neurofibromatosis (NF-1) who suffered with blindness suffered enucleation. Physical examination & histopathology were performed. Physical examination revealed Buphthalmos & vascularized cornea with lower lid ectropion and orbital deformity...

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Bibliographic Details
Main Authors: F. Asadi-Amoli, A. Ariapad S. Z. Tabatabaei
Format: Article
Language:English
Published: Tehran University of Medical Sciences 2007-09-01
Series:Acta Medica Iranica
Subjects:
Neurofibromatosis-1
plexiform neurofibroma
buphthalmos
enucleation
Online Access:http://journals.tums.ac.ir/PdfMed.aspx?pdf_med=/upload_files/pdf/5799.pdf&manuscript_id=5799
Description
Summary:To report a case of buphthalmos with neurofibromatosis (NF-1) who suffered with blindness suffered enucleation. Physical examination & histopathology were performed. Physical examination revealed Buphthalmos & vascularized cornea with lower lid ectropion and orbital deformity. Histopathologic findings shows plexiform neurofibroma in orbital tissue with scleral wall involvement. And hamartomatous proliferation in choroid & cilliary bodies with melanocytic elements. Few NF-1 cases with buphthalmos have been reported. But cases with complicationg buphthalmos (retinal Detachment & optic nerve Atrophy) suffering enucleation are very rare.
ISSN:0044-6025

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