Papillon-Lefevre Syndrome - A Report Of 2 Cases

Papillon-Lefevre syndrome is an inherited disorder of Keratinization characterized by palmoplantar keratoderma, associated with periodontosis and a tendency to frequent pyogenic skin infection. The clinical expression of this condition is highly variable. We report here, two cases of this rare syndr...

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Bibliographic Details
Main Authors: Gupta Shally, Kumar M Vijai, Thappa Devinder Mohan, Dave Shriya, Srikanth S, Thomas Shaji
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2002-01-01
Series:Indian Journal of Dermatology
Online Access:http://www.e-ijd.org/article.asp?issn=0019-5154;year=2002;volume=47;issue=1;spage=26;epage=28;aulast=Gupta;type=0
Description
Summary:Papillon-Lefevre syndrome is an inherited disorder of Keratinization characterized by palmoplantar keratoderma, associated with periodontosis and a tendency to frequent pyogenic skin infection. The clinical expression of this condition is highly variable. We report here, two cases of this rare syndrome occurring in 18 year old unmarried girl and a 54 year old married woman. Differentiating points from two recently described syndromes have been highlighted in the discussion.
ISSN:0019-5154
1998-3611