Systemic sclerosis: A rare cause of heart failure?

Systemic sclerosis (SS) is a chronic disease in which there may be multisystem involvement. It is rare (estimated prevalence: 0.5–2/10 000) with high morbidity and mortality, and there is as yet no curative treatment.We report the case of a young woman newly diagnosed with SS, in whom decompensated...

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Main Authors: María Cristina González-Cambeiro, Emad Abu-Assi, Rami Riziq-Yousef Abumuaileq, Sergio Raposeiras-Roubín, Pedro Rigueiro-Veloso, Alejandro Virgós-Lamela, Oscar Díaz-Castro, José Ramón González-Juanatey
Format: Article
Language:English
Published: Elsevier 2015-10-01
Series:Revista Portuguesa de Cardiologia
Online Access:http://www.sciencedirect.com/science/article/pii/S0870255115002176
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spelling doaj-1163405088d04040b1c93f9acc7157fb2020-11-25T02:47:46ZengElsevierRevista Portuguesa de Cardiologia0870-25512015-10-013410617.e1617.e5Systemic sclerosis: A rare cause of heart failure?María Cristina González-Cambeiro0Emad Abu-Assi1Rami Riziq-Yousef Abumuaileq2Sergio Raposeiras-Roubín3Pedro Rigueiro-Veloso4Alejandro Virgós-Lamela5Oscar Díaz-Castro6José Ramón González-Juanatey7Servicio de Cardiología y Unidad Coronaria, Hospital Clínico Universitario de Santiago de Compostela, Spain; Corresponding author.Servicio de Cardiología y Unidad Coronaria, Hospital Clínico Universitario de Santiago de Compostela, SpainServicio de Cardiología y Unidad Coronaria, Hospital Clínico Universitario de Santiago de Compostela, SpainServicio de Cardiología y Unidad Coronaria, Hospital Clínico Universitario de Santiago de Compostela, SpainServicio de Cardiología y Unidad Coronaria, Hospital Clínico Universitario de Santiago de Compostela, SpainServicio de Cardiología y Unidad Coronaria, Hospital Clínico Universitario de Santiago de Compostela, SpainServicio de Cardiología y Unidad Coronaria, Complejo Hospitalario de Pontevedra, SpainServicio de Cardiología y Unidad Coronaria, Hospital Clínico Universitario de Santiago de Compostela, SpainSystemic sclerosis (SS) is a chronic disease in which there may be multisystem involvement. It is rare (estimated prevalence: 0.5–2/10 000) with high morbidity and mortality, and there is as yet no curative treatment.We report the case of a young woman newly diagnosed with SS, in whom decompensated heart failure was the main manifestation. Resumo: A esclerose sistémica (ES) é uma doença crónica com possível apresentação multi-sistémica. É considerada uma doença rara (prevalência estimada: 0.5-2/10,000) com alta morbilidade e mortalidade para a qual não há cura hoje em dia.Relatamos o caso de uma jovem mulher, recém diagnosticada de ES por afetação pleural e cutânea, com insuficiência cardíaca global no momento da consulta. Keywords: Systemic sclerosis, Cardiomyopathy, Heart failure, Palavras-chave: Esclerose sistémica, Cardiomiopatia, Insuficiência cardíacahttp://www.sciencedirect.com/science/article/pii/S0870255115002176
collection DOAJ
language English
format Article
sources DOAJ
author María Cristina González-Cambeiro
Emad Abu-Assi
Rami Riziq-Yousef Abumuaileq
Sergio Raposeiras-Roubín
Pedro Rigueiro-Veloso
Alejandro Virgós-Lamela
Oscar Díaz-Castro
José Ramón González-Juanatey
spellingShingle María Cristina González-Cambeiro
Emad Abu-Assi
Rami Riziq-Yousef Abumuaileq
Sergio Raposeiras-Roubín
Pedro Rigueiro-Veloso
Alejandro Virgós-Lamela
Oscar Díaz-Castro
José Ramón González-Juanatey
Systemic sclerosis: A rare cause of heart failure?
Revista Portuguesa de Cardiologia
author_facet María Cristina González-Cambeiro
Emad Abu-Assi
Rami Riziq-Yousef Abumuaileq
Sergio Raposeiras-Roubín
Pedro Rigueiro-Veloso
Alejandro Virgós-Lamela
Oscar Díaz-Castro
José Ramón González-Juanatey
author_sort María Cristina González-Cambeiro
title Systemic sclerosis: A rare cause of heart failure?
title_short Systemic sclerosis: A rare cause of heart failure?
title_full Systemic sclerosis: A rare cause of heart failure?
title_fullStr Systemic sclerosis: A rare cause of heart failure?
title_full_unstemmed Systemic sclerosis: A rare cause of heart failure?
title_sort systemic sclerosis: a rare cause of heart failure?
publisher Elsevier
series Revista Portuguesa de Cardiologia
issn 0870-2551
publishDate 2015-10-01
description Systemic sclerosis (SS) is a chronic disease in which there may be multisystem involvement. It is rare (estimated prevalence: 0.5–2/10 000) with high morbidity and mortality, and there is as yet no curative treatment.We report the case of a young woman newly diagnosed with SS, in whom decompensated heart failure was the main manifestation. Resumo: A esclerose sistémica (ES) é uma doença crónica com possível apresentação multi-sistémica. É considerada uma doença rara (prevalência estimada: 0.5-2/10,000) com alta morbilidade e mortalidade para a qual não há cura hoje em dia.Relatamos o caso de uma jovem mulher, recém diagnosticada de ES por afetação pleural e cutânea, com insuficiência cardíaca global no momento da consulta. Keywords: Systemic sclerosis, Cardiomyopathy, Heart failure, Palavras-chave: Esclerose sistémica, Cardiomiopatia, Insuficiência cardíaca
url http://www.sciencedirect.com/science/article/pii/S0870255115002176
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