Granulomatosis (Wegener's granulomatosis) with polyangiitis presented as pulmonary manifestation: a case report
Abstract Pulmonary vasculitis can be the manifestation of several systemic illnesses such as primary systemic vasculitis, collagen vascular diseases, and systemic diseases associated with autoantibodies. It may be associated with granulomatous, eosinophilic, lymphoplasmacytic and neutrophilic inflam...
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doaj-130bfc9615f842aca4dc20db6c3229942020-11-25T03:41:36ZengWileyRespirology Case Reports2051-33802020-11-0188n/an/a10.1002/rcr2.674Granulomatosis (Wegener's granulomatosis) with polyangiitis presented as pulmonary manifestation: a case reportQusay Jummaa Lazim0Sinan Shakir Gheni Atrah1Khalid Jawad Mutlag2Haider Saadoon Qasim Alhilfi3Ahmed Muhi Fahad4Ahmed Salih Alshewered5Department of Cardiovascular Surgery Al‐Sadder Teaching Hospital, Misan Health Directorate, Ministry of Health/Environment Misan IraqDepartment of Radiology Al‐Sadder Teaching Hospital, Misan Health Directorate, Ministry of Health/ Environment Misan IraqDepartment of Rheumatology Al‐Sadder Teaching Hospital, Misan Health Directorate, Ministry of Health/ Environment Misan IraqFaculty of Medicine, Department of Medicine Misan University Misan IraqDepartment of Cardiovascular Surgery Al‐Sadder Teaching Hospital, Misan Health Directorate, Ministry of Health/Environment Misan IraqMisan Radiation Oncology Center Misan Health Directorate, Ministry of Health/Environment Misan IraqAbstract Pulmonary vasculitis can be the manifestation of several systemic illnesses such as primary systemic vasculitis, collagen vascular diseases, and systemic diseases associated with autoantibodies. It may be associated with granulomatous, eosinophilic, lymphoplasmacytic and neutrophilic inflammatory diseases. In this case report, we describe a 22‐year‐old female presented with intermittent fever, sweating and shivering, haemoptysis, sore throat, shortness of breath, fatigue, loss of appetite, nausea, non‐projectile vomiting, dizziness, and dark coloured urine. The diagnosis of granulomatosis with polyangiitis was made utilizing biochemical and radiological tests. Several pharmacological therapies were tried including rituximab. The patient made a good recovery and was discharged home after 12 days of hospitalization. The knowledge of the main radiographic and computed tomography (CT) scan findings, in association with clinical and laboratory data, often enables non‐invasive diagnosis of pulmonary vasculitis.https://doi.org/10.1002/rcr2.674Antineutrophil cytoplasmic antibodygranulomatosispolyangiitispulmonary vasculitisWegener's granulomatosis |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Qusay Jummaa Lazim Sinan Shakir Gheni Atrah Khalid Jawad Mutlag Haider Saadoon Qasim Alhilfi Ahmed Muhi Fahad Ahmed Salih Alshewered |
spellingShingle |
Qusay Jummaa Lazim Sinan Shakir Gheni Atrah Khalid Jawad Mutlag Haider Saadoon Qasim Alhilfi Ahmed Muhi Fahad Ahmed Salih Alshewered Granulomatosis (Wegener's granulomatosis) with polyangiitis presented as pulmonary manifestation: a case report Respirology Case Reports Antineutrophil cytoplasmic antibody granulomatosis polyangiitis pulmonary vasculitis Wegener's granulomatosis |
author_facet |
Qusay Jummaa Lazim Sinan Shakir Gheni Atrah Khalid Jawad Mutlag Haider Saadoon Qasim Alhilfi Ahmed Muhi Fahad Ahmed Salih Alshewered |
author_sort |
Qusay Jummaa Lazim |
title |
Granulomatosis (Wegener's granulomatosis) with polyangiitis presented as pulmonary manifestation: a case report |
title_short |
Granulomatosis (Wegener's granulomatosis) with polyangiitis presented as pulmonary manifestation: a case report |
title_full |
Granulomatosis (Wegener's granulomatosis) with polyangiitis presented as pulmonary manifestation: a case report |
title_fullStr |
Granulomatosis (Wegener's granulomatosis) with polyangiitis presented as pulmonary manifestation: a case report |
title_full_unstemmed |
Granulomatosis (Wegener's granulomatosis) with polyangiitis presented as pulmonary manifestation: a case report |
title_sort |
granulomatosis (wegener's granulomatosis) with polyangiitis presented as pulmonary manifestation: a case report |
publisher |
Wiley |
series |
Respirology Case Reports |
issn |
2051-3380 |
publishDate |
2020-11-01 |
description |
Abstract Pulmonary vasculitis can be the manifestation of several systemic illnesses such as primary systemic vasculitis, collagen vascular diseases, and systemic diseases associated with autoantibodies. It may be associated with granulomatous, eosinophilic, lymphoplasmacytic and neutrophilic inflammatory diseases. In this case report, we describe a 22‐year‐old female presented with intermittent fever, sweating and shivering, haemoptysis, sore throat, shortness of breath, fatigue, loss of appetite, nausea, non‐projectile vomiting, dizziness, and dark coloured urine. The diagnosis of granulomatosis with polyangiitis was made utilizing biochemical and radiological tests. Several pharmacological therapies were tried including rituximab. The patient made a good recovery and was discharged home after 12 days of hospitalization. The knowledge of the main radiographic and computed tomography (CT) scan findings, in association with clinical and laboratory data, often enables non‐invasive diagnosis of pulmonary vasculitis. |
topic |
Antineutrophil cytoplasmic antibody granulomatosis polyangiitis pulmonary vasculitis Wegener's granulomatosis |
url |
https://doi.org/10.1002/rcr2.674 |
work_keys_str_mv |
AT qusayjummaalazim granulomatosiswegenersgranulomatosiswithpolyangiitispresentedaspulmonarymanifestationacasereport AT sinanshakirgheniatrah granulomatosiswegenersgranulomatosiswithpolyangiitispresentedaspulmonarymanifestationacasereport AT khalidjawadmutlag granulomatosiswegenersgranulomatosiswithpolyangiitispresentedaspulmonarymanifestationacasereport AT haidersaadoonqasimalhilfi granulomatosiswegenersgranulomatosiswithpolyangiitispresentedaspulmonarymanifestationacasereport AT ahmedmuhifahad granulomatosiswegenersgranulomatosiswithpolyangiitispresentedaspulmonarymanifestationacasereport AT ahmedsalihalshewered granulomatosiswegenersgranulomatosiswithpolyangiitispresentedaspulmonarymanifestationacasereport |
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