Syndrome of right isomerism: Ivemark syndrome

Heterotaxy Syndrome is a complex syndrome that occurs when the axes of the body fail to rotate correctly when developing in the uterus. This can result in many different organ systems being affected. Cardiac malformations are a major component of heterotaxy syndrome, resulting in significant morbidi...

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Main Authors: Dipti Jain, Bhushan Chavan, Anita Manoj
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2018-01-01
Series:Journal of Mahatma Gandhi Institute of Medical Sciences
Subjects:
Online Access:http://www.jmgims.co.in/article.asp?issn=0971-9903;year=2018;volume=23;issue=2;spage=92;epage=94;aulast=Jain
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spelling doaj-16d12c96f2a24ae2b92a7fdbe7dc5a822020-11-24T22:09:21ZengWolters Kluwer Medknow PublicationsJournal of Mahatma Gandhi Institute of Medical Sciences0971-99032018-01-01232929410.4103/jmgims.jmgims_31_17Syndrome of right isomerism: Ivemark syndromeDipti JainBhushan ChavanAnita ManojHeterotaxy Syndrome is a complex syndrome that occurs when the axes of the body fail to rotate correctly when developing in the uterus. This can result in many different organ systems being affected. Cardiac malformations are a major component of heterotaxy syndrome, resulting in significant morbidity and mortality. Abnormal cardiac development typically leads to atrial appendage isomerism, resulting in either bilateral paired right atria (right atrial isomerism or paired left atria (left atrial isomerism. Here we present a one and a half-month-old female child with right isomerism.http://www.jmgims.co.in/article.asp?issn=0971-9903;year=2018;volume=23;issue=2;spage=92;epage=94;aulast=JainAspleniaIvemark syndromemultiple cardiac defects
collection DOAJ
language English
format Article
sources DOAJ
author Dipti Jain
Bhushan Chavan
Anita Manoj
spellingShingle Dipti Jain
Bhushan Chavan
Anita Manoj
Syndrome of right isomerism: Ivemark syndrome
Journal of Mahatma Gandhi Institute of Medical Sciences
Asplenia
Ivemark syndrome
multiple cardiac defects
author_facet Dipti Jain
Bhushan Chavan
Anita Manoj
author_sort Dipti Jain
title Syndrome of right isomerism: Ivemark syndrome
title_short Syndrome of right isomerism: Ivemark syndrome
title_full Syndrome of right isomerism: Ivemark syndrome
title_fullStr Syndrome of right isomerism: Ivemark syndrome
title_full_unstemmed Syndrome of right isomerism: Ivemark syndrome
title_sort syndrome of right isomerism: ivemark syndrome
publisher Wolters Kluwer Medknow Publications
series Journal of Mahatma Gandhi Institute of Medical Sciences
issn 0971-9903
publishDate 2018-01-01
description Heterotaxy Syndrome is a complex syndrome that occurs when the axes of the body fail to rotate correctly when developing in the uterus. This can result in many different organ systems being affected. Cardiac malformations are a major component of heterotaxy syndrome, resulting in significant morbidity and mortality. Abnormal cardiac development typically leads to atrial appendage isomerism, resulting in either bilateral paired right atria (right atrial isomerism or paired left atria (left atrial isomerism. Here we present a one and a half-month-old female child with right isomerism.
topic Asplenia
Ivemark syndrome
multiple cardiac defects
url http://www.jmgims.co.in/article.asp?issn=0971-9903;year=2018;volume=23;issue=2;spage=92;epage=94;aulast=Jain
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AT bhushanchavan syndromeofrightisomerismivemarksyndrome
AT anitamanoj syndromeofrightisomerismivemarksyndrome
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