Syndrome of right isomerism: Ivemark syndrome
Heterotaxy Syndrome is a complex syndrome that occurs when the axes of the body fail to rotate correctly when developing in the uterus. This can result in many different organ systems being affected. Cardiac malformations are a major component of heterotaxy syndrome, resulting in significant morbidi...
Main Authors: | , , |
---|---|
Format: | Article |
Language: | English |
Published: |
Wolters Kluwer Medknow Publications
2018-01-01
|
Series: | Journal of Mahatma Gandhi Institute of Medical Sciences |
Subjects: | |
Online Access: | http://www.jmgims.co.in/article.asp?issn=0971-9903;year=2018;volume=23;issue=2;spage=92;epage=94;aulast=Jain |
id |
doaj-16d12c96f2a24ae2b92a7fdbe7dc5a82 |
---|---|
record_format |
Article |
spelling |
doaj-16d12c96f2a24ae2b92a7fdbe7dc5a822020-11-24T22:09:21ZengWolters Kluwer Medknow PublicationsJournal of Mahatma Gandhi Institute of Medical Sciences0971-99032018-01-01232929410.4103/jmgims.jmgims_31_17Syndrome of right isomerism: Ivemark syndromeDipti JainBhushan ChavanAnita ManojHeterotaxy Syndrome is a complex syndrome that occurs when the axes of the body fail to rotate correctly when developing in the uterus. This can result in many different organ systems being affected. Cardiac malformations are a major component of heterotaxy syndrome, resulting in significant morbidity and mortality. Abnormal cardiac development typically leads to atrial appendage isomerism, resulting in either bilateral paired right atria (right atrial isomerism or paired left atria (left atrial isomerism. Here we present a one and a half-month-old female child with right isomerism.http://www.jmgims.co.in/article.asp?issn=0971-9903;year=2018;volume=23;issue=2;spage=92;epage=94;aulast=JainAspleniaIvemark syndromemultiple cardiac defects |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Dipti Jain Bhushan Chavan Anita Manoj |
spellingShingle |
Dipti Jain Bhushan Chavan Anita Manoj Syndrome of right isomerism: Ivemark syndrome Journal of Mahatma Gandhi Institute of Medical Sciences Asplenia Ivemark syndrome multiple cardiac defects |
author_facet |
Dipti Jain Bhushan Chavan Anita Manoj |
author_sort |
Dipti Jain |
title |
Syndrome of right isomerism: Ivemark syndrome |
title_short |
Syndrome of right isomerism: Ivemark syndrome |
title_full |
Syndrome of right isomerism: Ivemark syndrome |
title_fullStr |
Syndrome of right isomerism: Ivemark syndrome |
title_full_unstemmed |
Syndrome of right isomerism: Ivemark syndrome |
title_sort |
syndrome of right isomerism: ivemark syndrome |
publisher |
Wolters Kluwer Medknow Publications |
series |
Journal of Mahatma Gandhi Institute of Medical Sciences |
issn |
0971-9903 |
publishDate |
2018-01-01 |
description |
Heterotaxy Syndrome is a complex syndrome that occurs when the axes of the body fail to rotate correctly when developing in the uterus. This can result in many different organ systems being affected. Cardiac malformations are a major component of heterotaxy syndrome, resulting in significant morbidity and mortality. Abnormal cardiac development typically leads to atrial appendage isomerism, resulting in either bilateral paired right atria (right atrial isomerism or paired left atria (left atrial isomerism. Here we present a one and a half-month-old female child with right isomerism. |
topic |
Asplenia Ivemark syndrome multiple cardiac defects |
url |
http://www.jmgims.co.in/article.asp?issn=0971-9903;year=2018;volume=23;issue=2;spage=92;epage=94;aulast=Jain |
work_keys_str_mv |
AT diptijain syndromeofrightisomerismivemarksyndrome AT bhushanchavan syndromeofrightisomerismivemarksyndrome AT anitamanoj syndromeofrightisomerismivemarksyndrome |
_version_ |
1725812300562038784 |