| Summary: | Objective: To report the case of primary aortic angiosarcoma with bilateral adrenal metastasis coming with acute limb ischemia, including the management and pathological report.
Case presentation: A 54 year-old female came to the hospital because of her back pain. CTA of the whole aorta revealed the posterior mediastinal mass invaded the aorta, bilateral adrenal mass and renal infarction. She was sent for endoscopic ultrasonography (EUS) with fine needle aspiration (FNA) at the mediastinal mass and adrenal mass. During
the hospitalization, the patient developed acute limb ischemia on her right leg. CTA of the both legs showed absence of the distal run-off from the right common iliac artery. We performed femoral embolectomy and TEVAR. Pathological report showed malignant spindle cells and the immunohistochemistry suspected the angiosarcoma of the aorta.
Conclusion: Primary aortic angiosarcoma is a very rare disease. There is no consistent approach to the management due to its rarity.
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