Can spontaneous bifrontal extradural haematoma be a sole presentation in previously undiagnosed sickle cell disease? A rare case report and literature review
Background: Spontaneous epidural hematoma (EDH) is a rare entity with only few cases reported in literature. Spontaneous EDH can be due to dural vascular malformations, coagulopathies, sinus infections, middle ear or orbital infections and tumours. Although spontaneous EDH as a complication of sickl...
Main Authors: | , , |
---|---|
Format: | Article |
Language: | English |
Published: |
Elsevier
2021-09-01
|
Series: | Interdisciplinary Neurosurgery |
Subjects: | |
Online Access: | http://www.sciencedirect.com/science/article/pii/S2214751921001420 |
id |
doaj-1d3b422fb35448e082a867fd85e60b4b |
---|---|
record_format |
Article |
spelling |
doaj-1d3b422fb35448e082a867fd85e60b4b2021-07-17T04:34:15ZengElsevierInterdisciplinary Neurosurgery2214-75192021-09-0125101230Can spontaneous bifrontal extradural haematoma be a sole presentation in previously undiagnosed sickle cell disease? A rare case report and literature reviewManish Chaurasiya0Sandeep Bhardwaj1Devendra Naik2Department of Neurosurgery, Shri Balaji Super Speciality Hospital, Raipur, Chhattisgarh, IndiaDepartment of Neurosurgery, Advanced Neurology Superspeciality Hospital, Jaipur, Rajasthan, India; Corresponding author.Department of Surgery, Shri Balaji Super Speciality Hospital, Raipur, Chhattisgarh, IndiaBackground: Spontaneous epidural hematoma (EDH) is a rare entity with only few cases reported in literature. Spontaneous EDH can be due to dural vascular malformations, coagulopathies, sinus infections, middle ear or orbital infections and tumours. Although spontaneous EDH as a complication of sickle cell disease is even much rarer. Case report: Author reported a case of bifrontal spontaneous EDH in a 9 year old child who presented with severe headache and vomiting with GCS 12/15 (E3V4M5). NCCT head was done which was suggestive of bifrontal EDH with mass effect. Immediate craniotomy was done and epidural hematoma was evacuated. Patient made a successful recovery. He was later investigated and found to be suffering from sickle cell disease. Conclusion: This case report highlights that a previously asymptomatic sickle cell disease patient can present with spontaneous large epidural hematoma which requires immediate surgical intervention. So, this can be a sole presentation in sickle cell disease in previously asymptomatic patients. Sickle cell disease should always be kept in differential diagnosis in spontaneous extradural haematomas.http://www.sciencedirect.com/science/article/pii/S2214751921001420Spontaneous epidural hematomasSickle cell diseaseBifrontal craniotomy |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Manish Chaurasiya Sandeep Bhardwaj Devendra Naik |
spellingShingle |
Manish Chaurasiya Sandeep Bhardwaj Devendra Naik Can spontaneous bifrontal extradural haematoma be a sole presentation in previously undiagnosed sickle cell disease? A rare case report and literature review Interdisciplinary Neurosurgery Spontaneous epidural hematomas Sickle cell disease Bifrontal craniotomy |
author_facet |
Manish Chaurasiya Sandeep Bhardwaj Devendra Naik |
author_sort |
Manish Chaurasiya |
title |
Can spontaneous bifrontal extradural haematoma be a sole presentation in previously undiagnosed sickle cell disease? A rare case report and literature review |
title_short |
Can spontaneous bifrontal extradural haematoma be a sole presentation in previously undiagnosed sickle cell disease? A rare case report and literature review |
title_full |
Can spontaneous bifrontal extradural haematoma be a sole presentation in previously undiagnosed sickle cell disease? A rare case report and literature review |
title_fullStr |
Can spontaneous bifrontal extradural haematoma be a sole presentation in previously undiagnosed sickle cell disease? A rare case report and literature review |
title_full_unstemmed |
Can spontaneous bifrontal extradural haematoma be a sole presentation in previously undiagnosed sickle cell disease? A rare case report and literature review |
title_sort |
can spontaneous bifrontal extradural haematoma be a sole presentation in previously undiagnosed sickle cell disease? a rare case report and literature review |
publisher |
Elsevier |
series |
Interdisciplinary Neurosurgery |
issn |
2214-7519 |
publishDate |
2021-09-01 |
description |
Background: Spontaneous epidural hematoma (EDH) is a rare entity with only few cases reported in literature. Spontaneous EDH can be due to dural vascular malformations, coagulopathies, sinus infections, middle ear or orbital infections and tumours. Although spontaneous EDH as a complication of sickle cell disease is even much rarer. Case report: Author reported a case of bifrontal spontaneous EDH in a 9 year old child who presented with severe headache and vomiting with GCS 12/15 (E3V4M5). NCCT head was done which was suggestive of bifrontal EDH with mass effect. Immediate craniotomy was done and epidural hematoma was evacuated. Patient made a successful recovery. He was later investigated and found to be suffering from sickle cell disease. Conclusion: This case report highlights that a previously asymptomatic sickle cell disease patient can present with spontaneous large epidural hematoma which requires immediate surgical intervention. So, this can be a sole presentation in sickle cell disease in previously asymptomatic patients. Sickle cell disease should always be kept in differential diagnosis in spontaneous extradural haematomas. |
topic |
Spontaneous epidural hematomas Sickle cell disease Bifrontal craniotomy |
url |
http://www.sciencedirect.com/science/article/pii/S2214751921001420 |
work_keys_str_mv |
AT manishchaurasiya canspontaneousbifrontalextraduralhaematomabeasolepresentationinpreviouslyundiagnosedsicklecelldiseaseararecasereportandliteraturereview AT sandeepbhardwaj canspontaneousbifrontalextraduralhaematomabeasolepresentationinpreviouslyundiagnosedsicklecelldiseaseararecasereportandliteraturereview AT devendranaik canspontaneousbifrontalextraduralhaematomabeasolepresentationinpreviouslyundiagnosedsicklecelldiseaseararecasereportandliteraturereview |
_version_ |
1721296955510882304 |