Peroral Endoscopic Myotomy in Diffuse Thickened Esophageal Wall in an Adolescent

Peroral Endoscopic Myotomy in Diffuse Thickened Esophageal Wall in an Adolescent

Achalasia is an extremely rare pathology in children. Peroral endoscopic myotomy (POEM) is the gold standard for the surgical treatment of achalasia in adults, but only a limited number of cases of achalasia treatment using POEM in children have been published in the literature. Sometimes, high-reso...

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Bibliographic Details
Main Authors: Alexander A. Smirnov, Aleksandr N. Burakov, Aleksandr N. Shvetsov, Egor V. Blinov, Kirill D. Semenikhin, Nadezhda V. Konkina, Sergey Y. Dvoreckij
Format: Article
Language:English
Published: Karger Publishers 2018-08-01
Series:Case Reports in Gastroenterology
Subjects:
Diffuse esophageal wall thickening
Esophagus
Peroral endoscopic myotomy
Achalasia
Alport syndrome
Online Access:https://www.karger.com/Article/FullText/492212
Description
Summary:Achalasia is an extremely rare pathology in children. Peroral endoscopic myotomy (POEM) is the gold standard for the surgical treatment of achalasia in adults, but only a limited number of cases of achalasia treatment using POEM in children have been published in the literature. Sometimes, high-resolution manometry signs of achalasia can mimic diffuse esophageal leiomyoma. This case report represents the first known successful performance of POEM on a 15-year-old female with diffuse thickening of the esophagus with signs and symptoms of achalasia and suspicion for Alport syndrome associated with diffuse esophageal leiomyoma.
ISSN:1662-0631

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