Stenting of the right ventricular outflow tract after thrombosis of the modified Blalock-Taussig shunt in a 8 month old infant with tetralogy of Fallot and right pulmonary artery agenesis
Pulmonary artery agenesis combined with tetralogy of Fallot is the most rarely seen congenital heart disease. Children with this anomaly are an especially problematic category of patients undergoing staged surgical repair. The postoperative period quite often is complicated with shunt thrombosis whi...
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doaj-2095ba2899f749f9946342a90fa22b2e2021-07-28T21:11:22ZrusMONIKIAlʹmanah Kliničeskoj Mediciny2072-05052587-92942017-06-0145325425710.18786/2072-0505-2017-45-3-254-257455Stenting of the right ventricular outflow tract after thrombosis of the modified Blalock-Taussig shunt in a 8 month old infant with tetralogy of Fallot and right pulmonary artery agenesisI. A. Soynov0A. V. Gorbatykh1N. R. Nichay2A. Yu. Omel'chenko3A. V. Leykekhman4Yu. Yu. Kulyabin5A. V. Voytov6Yu. N. Gorbatykh7Academician E.N. Meshalkin Novosibirsk State Research Institute of Circulation PathologyAcademician E.N. Meshalkin Novosibirsk State Research Institute of Circulation PathologyAcademician E.N. Meshalkin Novosibirsk State Research Institute of Circulation PathologyAcademician E.N. Meshalkin Novosibirsk State Research Institute of Circulation PathologyAcademician E.N. Meshalkin Novosibirsk State Research Institute of Circulation PathologyAcademician E.N. Meshalkin Novosibirsk State Research Institute of Circulation PathologyAcademician E.N. Meshalkin Novosibirsk State Research Institute of Circulation PathologyAcademician E.N. Meshalkin Novosibirsk State Research Institute of Circulation PathologyPulmonary artery agenesis combined with tetralogy of Fallot is the most rarely seen congenital heart disease. Children with this anomaly are an especially problematic category of patients undergoing staged surgical repair. The postoperative period quite often is complicated with shunt thrombosis while a redo open surgery is associated with a very high risk; therefore, endovascular repair is a preferred procedure. We describe a case of right ventricular outflow tract stenting in a 8 month old girl with tetralogy of Fallot and right pulmonary artery agenesis. The patient was admitted at 3 month after performing of a left-sided modified Blalock-Taussig shunt with severe signs of heart failure and desaturation caused by shunt thrombosis. Assessments performed at 2 months after stenting of the outflow tract demonstrated good oxygen saturation in arterial blood (80% and above) and improvement of heart failure symptoms to NYHA II class.https://www.almclinmed.ru/jour/article/view/547tetralogy of fallotpulmonary artery agenesisright ventricular outflow tract stenting |
collection |
DOAJ |
language |
Russian |
format |
Article |
sources |
DOAJ |
author |
I. A. Soynov A. V. Gorbatykh N. R. Nichay A. Yu. Omel'chenko A. V. Leykekhman Yu. Yu. Kulyabin A. V. Voytov Yu. N. Gorbatykh |
spellingShingle |
I. A. Soynov A. V. Gorbatykh N. R. Nichay A. Yu. Omel'chenko A. V. Leykekhman Yu. Yu. Kulyabin A. V. Voytov Yu. N. Gorbatykh Stenting of the right ventricular outflow tract after thrombosis of the modified Blalock-Taussig shunt in a 8 month old infant with tetralogy of Fallot and right pulmonary artery agenesis Alʹmanah Kliničeskoj Mediciny tetralogy of fallot pulmonary artery agenesis right ventricular outflow tract stenting |
author_facet |
I. A. Soynov A. V. Gorbatykh N. R. Nichay A. Yu. Omel'chenko A. V. Leykekhman Yu. Yu. Kulyabin A. V. Voytov Yu. N. Gorbatykh |
author_sort |
I. A. Soynov |
title |
Stenting of the right ventricular outflow tract after thrombosis of the modified Blalock-Taussig shunt in a 8 month old infant with tetralogy of Fallot and right pulmonary artery agenesis |
title_short |
Stenting of the right ventricular outflow tract after thrombosis of the modified Blalock-Taussig shunt in a 8 month old infant with tetralogy of Fallot and right pulmonary artery agenesis |
title_full |
Stenting of the right ventricular outflow tract after thrombosis of the modified Blalock-Taussig shunt in a 8 month old infant with tetralogy of Fallot and right pulmonary artery agenesis |
title_fullStr |
Stenting of the right ventricular outflow tract after thrombosis of the modified Blalock-Taussig shunt in a 8 month old infant with tetralogy of Fallot and right pulmonary artery agenesis |
title_full_unstemmed |
Stenting of the right ventricular outflow tract after thrombosis of the modified Blalock-Taussig shunt in a 8 month old infant with tetralogy of Fallot and right pulmonary artery agenesis |
title_sort |
stenting of the right ventricular outflow tract after thrombosis of the modified blalock-taussig shunt in a 8 month old infant with tetralogy of fallot and right pulmonary artery agenesis |
publisher |
MONIKI |
series |
Alʹmanah Kliničeskoj Mediciny |
issn |
2072-0505 2587-9294 |
publishDate |
2017-06-01 |
description |
Pulmonary artery agenesis combined with tetralogy of Fallot is the most rarely seen congenital heart disease. Children with this anomaly are an especially problematic category of patients undergoing staged surgical repair. The postoperative period quite often is complicated with shunt thrombosis while a redo open surgery is associated with a very high risk; therefore, endovascular repair is a preferred procedure. We describe a case of right ventricular outflow tract stenting in a 8 month old girl with tetralogy of Fallot and right pulmonary artery agenesis. The patient was admitted at 3 month after performing of a left-sided modified Blalock-Taussig shunt with severe signs of heart failure and desaturation caused by shunt thrombosis. Assessments performed at 2 months after stenting of the outflow tract demonstrated good oxygen saturation in arterial blood (80% and above) and improvement of heart failure symptoms to NYHA II class. |
topic |
tetralogy of fallot pulmonary artery agenesis right ventricular outflow tract stenting |
url |
https://www.almclinmed.ru/jour/article/view/547 |
work_keys_str_mv |
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