Mitochondrial Dysfunction in Lysosomal Storage Disorders
Lysosomal storage diseases (LSDs) describe a heterogeneous group of rare inherited metabolic disorders that result from the absence or loss of function of lysosomal hydrolases or transporters, resulting in the progressive accumulation of undigested material in lysosomes. The accumulation of substanc...
Main Authors: | Mario de la Mata, David Cotán, Marina Villanueva-Paz, Isabel de Lavera, Mónica Álvarez-Córdoba, Raquel Luzón-Hidalgo, Juan M. Suárez-Rivero, Gustavo Tiscornia, Manuel Oropesa-Ávila |
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Format: | Article |
Language: | English |
Published: |
MDPI AG
2016-10-01
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Series: | Diseases |
Subjects: | |
Online Access: | http://www.mdpi.com/2079-9721/4/4/31 |
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