Reduced Granule Cell Proliferation and Molecular Dysregulation in the Cerebellum of Lysosomal Acid Phosphatase 2 (ACP2) Mutant Mice
Lysosomal acid phosphatase 2 (<i>Acp2</i>) mutant mice (naked-ataxia, <i>nax</i>) have a severe cerebellar cortex defect with a striking reduction in the number of granule cells. Using a combination of in vivo and in vitro immunohistochemistry, Western blotting, BrdU assays,...
Main Authors: | Xiaodan Jiao, Maryam Rahimi Balaei, Ejlal Abu-El-Rub, Filippo Casoni, Hassan Pezeshgi Modarres, Sanjiv Dhingra, Jiming Kong, Giacomo G. Consalez, Hassan Marzban |
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Format: | Article |
Language: | English |
Published: |
MDPI AG
2021-03-01
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Series: | International Journal of Molecular Sciences |
Subjects: | |
Online Access: | https://www.mdpi.com/1422-0067/22/6/2994 |
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