Isolated persistence of the fifth aortic arch in an infant presenting with congestive heart failure
The persistence of the fifth aortic arch (PFAA) in postnatal life is an extremely rare and controversial cardiovascular malformation. PFAA is defined as an extra-pericardial vessel arising from the ascending aorta proximal to the origin of the brachiocephalic arteries, terminating either in the dors...
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doaj-23cc4de0754e4f5e9625c739ef2f10072020-11-25T01:20:44ZengWolters Kluwer Medknow PublicationsAnnals of Pediatric Cardiology0974-20692020-01-01131919410.4103/apc.APC_53_19Isolated persistence of the fifth aortic arch in an infant presenting with congestive heart failureGiovanni MeliotaMaristella LombardiPierluigi ZazaMaria Rosaria TaglientePaolo VersacciGabriele ScalzoUgo VairoThe persistence of the fifth aortic arch (PFAA) in postnatal life is an extremely rare and controversial cardiovascular malformation. PFAA is defined as an extra-pericardial vessel arising from the ascending aorta proximal to the origin of the brachiocephalic arteries, terminating either in the dorsal aorta or in the pulmonary arteries through the persistently patent arterial duct. An isolated PFAA with systemic-to-pulmonary connection best fits this definition, while the vast majority of cases reported as PFAA may have alternative embryological explanations. We present a unique case of a 5-week-old patient with an isolated PFAA with systemic-to-pulmonary connection, who presented with congestive heart failure. A first differential diagnosis was made with distal aortopulmonary window and an atypical patent arterial duct. A careful analysis of the case and a systematic review of the literature made us conclude for an isolated PFAA, which is one of the only five cases ever reported.http://www.annalspc.com/article.asp?issn=0974-2069;year=2020;volume=13;issue=1;spage=91;epage=94;aulast=Meliotaaortic arch anomaliesaortopulmonary windowcongestive heart failurepersistence of fifth aortic arch |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Giovanni Meliota Maristella Lombardi Pierluigi Zaza Maria Rosaria Tagliente Paolo Versacci Gabriele Scalzo Ugo Vairo |
spellingShingle |
Giovanni Meliota Maristella Lombardi Pierluigi Zaza Maria Rosaria Tagliente Paolo Versacci Gabriele Scalzo Ugo Vairo Isolated persistence of the fifth aortic arch in an infant presenting with congestive heart failure Annals of Pediatric Cardiology aortic arch anomalies aortopulmonary window congestive heart failure persistence of fifth aortic arch |
author_facet |
Giovanni Meliota Maristella Lombardi Pierluigi Zaza Maria Rosaria Tagliente Paolo Versacci Gabriele Scalzo Ugo Vairo |
author_sort |
Giovanni Meliota |
title |
Isolated persistence of the fifth aortic arch in an infant presenting with congestive heart failure |
title_short |
Isolated persistence of the fifth aortic arch in an infant presenting with congestive heart failure |
title_full |
Isolated persistence of the fifth aortic arch in an infant presenting with congestive heart failure |
title_fullStr |
Isolated persistence of the fifth aortic arch in an infant presenting with congestive heart failure |
title_full_unstemmed |
Isolated persistence of the fifth aortic arch in an infant presenting with congestive heart failure |
title_sort |
isolated persistence of the fifth aortic arch in an infant presenting with congestive heart failure |
publisher |
Wolters Kluwer Medknow Publications |
series |
Annals of Pediatric Cardiology |
issn |
0974-2069 |
publishDate |
2020-01-01 |
description |
The persistence of the fifth aortic arch (PFAA) in postnatal life is an extremely rare and controversial cardiovascular malformation. PFAA is defined as an extra-pericardial vessel arising from the ascending aorta proximal to the origin of the brachiocephalic arteries, terminating either in the dorsal aorta or in the pulmonary arteries through the persistently patent arterial duct. An isolated PFAA with systemic-to-pulmonary connection best fits this definition, while the vast majority of cases reported as PFAA may have alternative embryological explanations. We present a unique case of a 5-week-old patient with an isolated PFAA with systemic-to-pulmonary connection, who presented with congestive heart failure. A first differential diagnosis was made with distal aortopulmonary window and an atypical patent arterial duct. A careful analysis of the case and a systematic review of the literature made us conclude for an isolated PFAA, which is one of the only five cases ever reported. |
topic |
aortic arch anomalies aortopulmonary window congestive heart failure persistence of fifth aortic arch |
url |
http://www.annalspc.com/article.asp?issn=0974-2069;year=2020;volume=13;issue=1;spage=91;epage=94;aulast=Meliota |
work_keys_str_mv |
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