Epidermal Nevus Syndrome and Dysplatic Kidney Disease

Epidermal nevus syndrome is a rare congenital disorder, characterized by epidermal nevi and multiple organ involvement. Multicystic kidney disease has been very rarely reported in this syndrome. Here is the report of a boy presented with multiple epidermal nevi, cardiac anomaly, seizure attack, hem...

Full description

Bibliographic Details
Main Authors:	Azar Nickavar, Najmessadat Atefi, Kambiz Kamyab Hesari
Format:	Article
Language:	English
Published:	Tehran University of Medical Sciences 2014-08-01
Series:	Acta Medica Iranica
Subjects:	Epidermal nevus syndrome Multicystic dysplastic kidney Wilms' tumor Neurocutaneous
Online Access:	https://acta.tums.ac.ir/index.php/acta/article/view/4558

id	doaj-24e118a52a804ad9a35261a039376fa3
record_format	Article
spelling	doaj-24e118a52a804ad9a35261a039376fa32020-11-25T03:26:02ZengTehran University of Medical SciencesActa Medica Iranica0044-60251735-96942014-08-015284511Epidermal Nevus Syndrome and Dysplatic Kidney DiseaseAzar Nickavar0Najmessadat Atefi1Kambiz Kamyab Hesari2Department of Pediatric Nephrology, Aliasghar Children's Hospital, Iran University of Medical Sciences, Tehran, Iran.Department of Dermatology, Aliasghar Children's Hospital, Iran University of Medical Sciences, Tehran, Iran.Department of Pathology, Razi Dermatology Hospital, Tehran University of Medical Sciences, Tehran, Iran. Epidermal nevus syndrome is a rare congenital disorder, characterized by epidermal nevi and multiple organ involvement. Multicystic kidney disease has been very rarely reported in this syndrome. Here is the report of a boy presented with multiple epidermal nevi, cardiac anomaly, seizure attack, hemi hypertrophy, and multicystic dysplastic kidney complicated with Wilms' tumor. According to this association, it is suggested to search for dysplastic kidney disease in patients with neurocutaneous disorders. https://acta.tums.ac.ir/index.php/acta/article/view/4558Epidermal nevus syndromeMulticystic dysplastic kidneyWilms' tumorNeurocutaneous
collection	DOAJ
language	English
format	Article
sources	DOAJ
author	Azar Nickavar Najmessadat Atefi Kambiz Kamyab Hesari
spellingShingle	Azar Nickavar Najmessadat Atefi Kambiz Kamyab Hesari Epidermal Nevus Syndrome and Dysplatic Kidney Disease Acta Medica Iranica Epidermal nevus syndrome Multicystic dysplastic kidney Wilms' tumor Neurocutaneous
author_facet	Azar Nickavar Najmessadat Atefi Kambiz Kamyab Hesari
author_sort	Azar Nickavar
title	Epidermal Nevus Syndrome and Dysplatic Kidney Disease
title_short	Epidermal Nevus Syndrome and Dysplatic Kidney Disease
title_full	Epidermal Nevus Syndrome and Dysplatic Kidney Disease
title_fullStr	Epidermal Nevus Syndrome and Dysplatic Kidney Disease
title_full_unstemmed	Epidermal Nevus Syndrome and Dysplatic Kidney Disease
title_sort	epidermal nevus syndrome and dysplatic kidney disease
publisher	Tehran University of Medical Sciences
series	Acta Medica Iranica
issn	0044-6025 1735-9694
publishDate	2014-08-01
description	Epidermal nevus syndrome is a rare congenital disorder, characterized by epidermal nevi and multiple organ involvement. Multicystic kidney disease has been very rarely reported in this syndrome. Here is the report of a boy presented with multiple epidermal nevi, cardiac anomaly, seizure attack, hemi hypertrophy, and multicystic dysplastic kidney complicated with Wilms' tumor. According to this association, it is suggested to search for dysplastic kidney disease in patients with neurocutaneous disorders.
topic	Epidermal nevus syndrome Multicystic dysplastic kidney Wilms' tumor Neurocutaneous
url	https://acta.tums.ac.ir/index.php/acta/article/view/4558
work_keys_str_mv	AT azarnickavar epidermalnevussyndromeanddysplatickidneydisease AT najmessadatatefi epidermalnevussyndromeanddysplatickidneydisease AT kambizkamyabhesari epidermalnevussyndromeanddysplatickidneydisease
_version_	1724594298910932992

Epidermal Nevus Syndrome and Dysplatic Kidney Disease

Similar Items