Epidermal Nevus Syndrome and Dysplatic Kidney Disease
Epidermal nevus syndrome is a rare congenital disorder, characterized by epidermal nevi and multiple organ involvement. Multicystic kidney disease has been very rarely reported in this syndrome. Here is the report of a boy presented with multiple epidermal nevi, cardiac anomaly, seizure attack, hem...
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Tehran University of Medical Sciences
2014-08-01
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doaj-24e118a52a804ad9a35261a039376fa32020-11-25T03:26:02ZengTehran University of Medical SciencesActa Medica Iranica0044-60251735-96942014-08-015284511Epidermal Nevus Syndrome and Dysplatic Kidney DiseaseAzar Nickavar0Najmessadat Atefi1Kambiz Kamyab Hesari2Department of Pediatric Nephrology, Aliasghar Children's Hospital, Iran University of Medical Sciences, Tehran, Iran.Department of Dermatology, Aliasghar Children's Hospital, Iran University of Medical Sciences, Tehran, Iran.Department of Pathology, Razi Dermatology Hospital, Tehran University of Medical Sciences, Tehran, Iran. Epidermal nevus syndrome is a rare congenital disorder, characterized by epidermal nevi and multiple organ involvement. Multicystic kidney disease has been very rarely reported in this syndrome. Here is the report of a boy presented with multiple epidermal nevi, cardiac anomaly, seizure attack, hemi hypertrophy, and multicystic dysplastic kidney complicated with Wilms' tumor. According to this association, it is suggested to search for dysplastic kidney disease in patients with neurocutaneous disorders. https://acta.tums.ac.ir/index.php/acta/article/view/4558Epidermal nevus syndromeMulticystic dysplastic kidneyWilms' tumorNeurocutaneous |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Azar Nickavar Najmessadat Atefi Kambiz Kamyab Hesari |
spellingShingle |
Azar Nickavar Najmessadat Atefi Kambiz Kamyab Hesari Epidermal Nevus Syndrome and Dysplatic Kidney Disease Acta Medica Iranica Epidermal nevus syndrome Multicystic dysplastic kidney Wilms' tumor Neurocutaneous |
author_facet |
Azar Nickavar Najmessadat Atefi Kambiz Kamyab Hesari |
author_sort |
Azar Nickavar |
title |
Epidermal Nevus Syndrome and Dysplatic Kidney Disease |
title_short |
Epidermal Nevus Syndrome and Dysplatic Kidney Disease |
title_full |
Epidermal Nevus Syndrome and Dysplatic Kidney Disease |
title_fullStr |
Epidermal Nevus Syndrome and Dysplatic Kidney Disease |
title_full_unstemmed |
Epidermal Nevus Syndrome and Dysplatic Kidney Disease |
title_sort |
epidermal nevus syndrome and dysplatic kidney disease |
publisher |
Tehran University of Medical Sciences |
series |
Acta Medica Iranica |
issn |
0044-6025 1735-9694 |
publishDate |
2014-08-01 |
description |
Epidermal nevus syndrome is a rare congenital disorder, characterized by epidermal nevi and multiple organ involvement. Multicystic kidney disease has been very rarely reported in this syndrome. Here is the report of a boy presented with multiple epidermal nevi, cardiac anomaly, seizure attack, hemi hypertrophy, and multicystic dysplastic kidney complicated with Wilms' tumor. According to this association, it is suggested to search for dysplastic kidney disease in patients with neurocutaneous disorders.
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topic |
Epidermal nevus syndrome Multicystic dysplastic kidney Wilms' tumor Neurocutaneous |
url |
https://acta.tums.ac.ir/index.php/acta/article/view/4558 |
work_keys_str_mv |
AT azarnickavar epidermalnevussyndromeanddysplatickidneydisease AT najmessadatatefi epidermalnevussyndromeanddysplatickidneydisease AT kambizkamyabhesari epidermalnevussyndromeanddysplatickidneydisease |
_version_ |
1724594298910932992 |