Suprarenal Wilms tumour with intraspinal metastases: An uncommon presentation of a common tumour

Wilms tumour is the commonest renal tumour in children with peak age group of 2–5 years [1,2]. It commonly presents as an incidentally detected abdominal mass; however fever, hematuria and hypertension may also be seen [1]. Extra-renal Wilms tumour is extremely rare, with an incidence of 0.5%–1% [3,...

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Bibliographic Details
Main Authors: Sneha Tandon, Maya Prasad, Mukta Ramadwar, Seema Kembhavi, Sneha Shah, Sajid Qureshi, Siddharth Laskar, Girish Chinnaswamy
Format: Article
Language:English
Published: Elsevier 2020-09-01
Series:Pediatric Hematology Oncology Journal
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Online Access:http://www.sciencedirect.com/science/article/pii/S2468124520300528
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Summary:Wilms tumour is the commonest renal tumour in children with peak age group of 2–5 years [1,2]. It commonly presents as an incidentally detected abdominal mass; however fever, hematuria and hypertension may also be seen [1]. Extra-renal Wilms tumour is extremely rare, with an incidence of 0.5%–1% [3,4]. Wilms tumour, most commonly metastasizes to the lungs, followed by lymph nodes and liver, however, metastasis to the bones and spinal cord at diagnosis is extremely rare [1,2,5–10]. We hereby, report an extremely rare presentation of suprarenal Wilms tumour with intraspinal metastases. Our case highlights the high degree of vigilance as well as timely intervention with multimodality therapy required to improve the outcomes in the setting of advanced metastatic disease; notwithstanding the potentially irreversible neurological weakness in the absence of optimal intervention.
ISSN:2468-1245