Ebstein's anomaly with imperforate tricuspid valve. Prenatal diagnosis

Ebstein's anomaly is an uncommon congenital heart defect, with a prevalence of 0.3-0.5%. Its association with an imperforate tricuspid valve is an even more rare situation (less than 10% of cases). Prenatal diagnosis of this association by means of fetal echocardiography has not been reported....

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Bibliographic Details
Main Authors: Zielinsky Paulo, Pilla Carlo B.
Format: Article
Language:English
Published: Sociedade Brasileira de Cardiologia (SBC) 2000-01-01
Series:Arquivos Brasileiros de Cardiologia
Online Access:http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0066-782X2000000700006
Description
Summary:Ebstein's anomaly is an uncommon congenital heart defect, with a prevalence of 0.3-0.5%. Its association with an imperforate tricuspid valve is an even more rare situation (less than 10% of cases). Prenatal diagnosis of this association by means of fetal echocardiography has not been reported. We describe here this association diagnosed before birth and confirmed after birth. The diagnostic potential and importance of fetal echocardiography during prenatal evaluation of cardiac malformations allows for adequate perinatal planning and management, with an obvious impact on morbidity and mortality.
ISSN:0066-782X
1678-4170