Congenital Complete Atrioventricular Block and Dilated Cardiomyopathy: New Light for an Old Disease

We present a case of a patient with known complete congenital atrioventricular block (CAVB) since the age of 7 years old that developed dilated cardiomyopathy ten years after VVI-R pacemaker implantation. He presented severe biventricular dysfunction and was symptomatic despite optimal medical ther...

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Main Authors: Mariana Paiva, Vania Ribeiro, Raquel Garcia, Sandra Amorim, Manuel Campelo, Elisabete Martins, Brenda Moura, Jose Cardoso, M. Júlia Maciel
Format: Article
Language:English
Published: Hindawi Limited 2012-01-01
Series:Case Reports in Cardiology
Online Access:http://dx.doi.org/10.1155/2012/451375
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spelling doaj-366347a8e1604938b658092799d84f482020-11-24T23:45:20ZengHindawi LimitedCase Reports in Cardiology2090-64042090-64122012-01-01201210.1155/2012/451375451375Congenital Complete Atrioventricular Block and Dilated Cardiomyopathy: New Light for an Old DiseaseMariana Paiva0Vania Ribeiro1Raquel Garcia2Sandra Amorim3Manuel Campelo4Elisabete Martins5Brenda Moura6Jose Cardoso7M. Júlia Maciel8Cardiology Department, Centro Hospitalar São João, 4200-319 Porto, PortugalCardiology Department, Centro Hospitalar São João, 4200-319 Porto, PortugalCardiology Department, Centro Hospitalar São João, 4200-319 Porto, PortugalCardiology Department, Centro Hospitalar São João, 4200-319 Porto, PortugalCardiology Department, Centro Hospitalar São João, 4200-319 Porto, PortugalCardiology Department, Centro Hospitalar São João, 4200-319 Porto, PortugalCardiology Department, Centro Hospitalar São João, 4200-319 Porto, PortugalCardiology Department, Centro Hospitalar São João, 4200-319 Porto, PortugalCardiology Department, Centro Hospitalar São João, 4200-319 Porto, PortugalWe present a case of a patient with known complete congenital atrioventricular block (CAVB) since the age of 7 years old that developed dilated cardiomyopathy ten years after VVI-R pacemaker implantation. He presented severe biventricular dysfunction and was symptomatic despite optimal medical therapy. Cardiac resynchronization therapy was used, and he showed clinical and electrocardiographic improvement a month later.http://dx.doi.org/10.1155/2012/451375
collection DOAJ
language English
format Article
sources DOAJ
author Mariana Paiva
Vania Ribeiro
Raquel Garcia
Sandra Amorim
Manuel Campelo
Elisabete Martins
Brenda Moura
Jose Cardoso
M. Júlia Maciel
spellingShingle Mariana Paiva
Vania Ribeiro
Raquel Garcia
Sandra Amorim
Manuel Campelo
Elisabete Martins
Brenda Moura
Jose Cardoso
M. Júlia Maciel
Congenital Complete Atrioventricular Block and Dilated Cardiomyopathy: New Light for an Old Disease
Case Reports in Cardiology
author_facet Mariana Paiva
Vania Ribeiro
Raquel Garcia
Sandra Amorim
Manuel Campelo
Elisabete Martins
Brenda Moura
Jose Cardoso
M. Júlia Maciel
author_sort Mariana Paiva
title Congenital Complete Atrioventricular Block and Dilated Cardiomyopathy: New Light for an Old Disease
title_short Congenital Complete Atrioventricular Block and Dilated Cardiomyopathy: New Light for an Old Disease
title_full Congenital Complete Atrioventricular Block and Dilated Cardiomyopathy: New Light for an Old Disease
title_fullStr Congenital Complete Atrioventricular Block and Dilated Cardiomyopathy: New Light for an Old Disease
title_full_unstemmed Congenital Complete Atrioventricular Block and Dilated Cardiomyopathy: New Light for an Old Disease
title_sort congenital complete atrioventricular block and dilated cardiomyopathy: new light for an old disease
publisher Hindawi Limited
series Case Reports in Cardiology
issn 2090-6404
2090-6412
publishDate 2012-01-01
description We present a case of a patient with known complete congenital atrioventricular block (CAVB) since the age of 7 years old that developed dilated cardiomyopathy ten years after VVI-R pacemaker implantation. He presented severe biventricular dysfunction and was symptomatic despite optimal medical therapy. Cardiac resynchronization therapy was used, and he showed clinical and electrocardiographic improvement a month later.
url http://dx.doi.org/10.1155/2012/451375
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