Gadolinium Chloride Rescues Niemann–Pick Type C Liver Damage

Gadolinium Chloride Rescues Niemann–Pick Type C Liver Damage

Niemann⁻Pick type C (NPC) disease is a rare neurovisceral cholesterol storage disorder that arises from loss of function mutations in the <i>NPC1</i> or <i>NPC2</i> genes. Soon after birth, some patients present with an aggressive hepatosplenomegaly and cholestatic...

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Bibliographic Details
Main Authors:	Andrés D. Klein, Juan Esteban Oyarzún, Cristian Cortez, Silvana Zanlungo
Format:	Article
Language:	English
Published:	MDPI AG 2018-11-01
Series:	International Journal of Molecular Sciences
Subjects:	Niemann–Pick type C disease gadolinium chloride liver disease cholesterol therapeutic option
Online Access:	https://www.mdpi.com/1422-0067/19/11/3599

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