Type I Chiari malformation presenting orthostatic syncope who treated with decompressive surgery
Chiari malformations are a congenital anomaly of the hindbrain. The most common, Chiari malformation type I (CM-I), is characterized by herniation of the cerebellar tonsils extending at least 3 mm below the plane of the foramen magnum. Consequently, CM-I is associated with hydrocephalus and symptoms...
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doaj-41972aeca26f4fe1850e1e5d2e7567d82020-11-24T20:45:58ZengKorean Pediatric SocietyKorean Journal of Pediatrics1738-10612092-72582016-11-0159Suppl 1S149S15110.3345/kjp.2016.59.11.S14920125553423Type I Chiari malformation presenting orthostatic syncope who treated with decompressive surgeryHyun-Seung Shin0Jeong A Kim1Dong-Seok Kim2Joon Soo Lee3Department of Pediatrics, Severance Children's Hospital, Yonsei University College of Medicine, Seoul, Korea.Division of Pediatric Neurology, Department of Pediatrics, Severance Children's Hospital, Yonsei University College of Medicine, Seoul, Korea.Department of Neurosurgery, Severance Hospital, Yonsei University College of Medicine, Seoul, Korea.Division of Pediatric Neurology, Department of Pediatrics, Severance Children's Hospital, Yonsei University College of Medicine, Seoul, Korea.Chiari malformations are a congenital anomaly of the hindbrain. The most common, Chiari malformation type I (CM-I), is characterized by herniation of the cerebellar tonsils extending at least 3 mm below the plane of the foramen magnum. Consequently, CM-I is associated with hydrocephalus and symptoms involving compression of the cervicomedullary junction by ectopic tonsils. Several studies have reported the clinical symptoms associated with CM-I, including suboccipital headache, weakness in the upper extremities, facial numbness, loss of temperature sensation, ataxia, diplopia, dysarthria, dysphagia, vomiting, vertigo, nystagmus, and tinnitus. Syncope is one of the rarest presentations in patients with CM-I. There are many hypotheses regarding the causes of syncope in patients with CM-I; however, the mechanisms are not clearly understood. Although surgical decompression for CM-I in patients with syncope has yielded good clinical results in some studies, such cases are rarely reported. We report a case of orthostatic syncope in a patient with CM-I who was treated with surgical intervention.http://kjp.or.kr/upload/pdf/kjped-59-S149.pdfChiari malformation type ISyncopeOrthostatic hypotension |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Hyun-Seung Shin Jeong A Kim Dong-Seok Kim Joon Soo Lee |
spellingShingle |
Hyun-Seung Shin Jeong A Kim Dong-Seok Kim Joon Soo Lee Type I Chiari malformation presenting orthostatic syncope who treated with decompressive surgery Korean Journal of Pediatrics Chiari malformation type I Syncope Orthostatic hypotension |
author_facet |
Hyun-Seung Shin Jeong A Kim Dong-Seok Kim Joon Soo Lee |
author_sort |
Hyun-Seung Shin |
title |
Type I Chiari malformation presenting orthostatic syncope who treated with decompressive surgery |
title_short |
Type I Chiari malformation presenting orthostatic syncope who treated with decompressive surgery |
title_full |
Type I Chiari malformation presenting orthostatic syncope who treated with decompressive surgery |
title_fullStr |
Type I Chiari malformation presenting orthostatic syncope who treated with decompressive surgery |
title_full_unstemmed |
Type I Chiari malformation presenting orthostatic syncope who treated with decompressive surgery |
title_sort |
type i chiari malformation presenting orthostatic syncope who treated with decompressive surgery |
publisher |
Korean Pediatric Society |
series |
Korean Journal of Pediatrics |
issn |
1738-1061 2092-7258 |
publishDate |
2016-11-01 |
description |
Chiari malformations are a congenital anomaly of the hindbrain. The most common, Chiari malformation type I (CM-I), is characterized by herniation of the cerebellar tonsils extending at least 3 mm below the plane of the foramen magnum. Consequently, CM-I is associated with hydrocephalus and symptoms involving compression of the cervicomedullary junction by ectopic tonsils. Several studies have reported the clinical symptoms associated with CM-I, including suboccipital headache, weakness in the upper extremities, facial numbness, loss of temperature sensation, ataxia, diplopia, dysarthria, dysphagia, vomiting, vertigo, nystagmus, and tinnitus. Syncope is one of the rarest presentations in patients with CM-I. There are many hypotheses regarding the causes of syncope in patients with CM-I; however, the mechanisms are not clearly understood. Although surgical decompression for CM-I in patients with syncope has yielded good clinical results in some studies, such cases are rarely reported. We report a case of orthostatic syncope in a patient with CM-I who was treated with surgical intervention. |
topic |
Chiari malformation type I Syncope Orthostatic hypotension |
url |
http://kjp.or.kr/upload/pdf/kjped-59-S149.pdf |
work_keys_str_mv |
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