Churg-Strauss Syndrome or Eosinophilic Granulomatosis with Polyangiitis: Exuberant Classic Clinical Picture of a Rare Disease

The authors present a classic case of Churg-Strauss syndrome with an exuberant clinical picture in a 34-year-old woman. She showed the following diagnostic criteria: asthma, polyneuropathy, rhinopathy, marked eosinophilia, positive p-ANCA with a perinuclear pattern, and skin histopathology results s...

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Main Authors: Luana Vieira Mukamal, Celso Tavares Sodré, Lara Beatriz Prata, Fernanda Nakasato, Tullia Cuzzi, Marcia Ramos-e-Silva
Format: Article
Language:English
Published: Karger Publishers 2018-06-01
Series:Case Reports in Dermatology
Subjects:
Online Access:https://www.karger.com/Article/FullText/489162
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spelling doaj-41fefa409a1a4d76b028ed245754b2ad2020-11-24T21:19:07ZengKarger PublishersCase Reports in Dermatology1662-65672018-06-0110217518110.1159/000489162489162Churg-Strauss Syndrome or Eosinophilic Granulomatosis with Polyangiitis: Exuberant Classic Clinical Picture of a Rare DiseaseLuana Vieira MukamalCelso Tavares SodréLara Beatriz PrataFernanda NakasatoTullia CuzziMarcia Ramos-e-SilvaThe authors present a classic case of Churg-Strauss syndrome with an exuberant clinical picture in a 34-year-old woman. She showed the following diagnostic criteria: asthma, polyneuropathy, rhinopathy, marked eosinophilia, positive p-ANCA with a perinuclear pattern, and skin histopathology results suggestive of vasculitis with eosinophils. There was a good response to prednisone, dexamethasone pulse therapy, and cyclophosphamide.https://www.karger.com/Article/FullText/489162Churg-Strauss syndromeAllergic granulomatous angiitisVasculitis
collection DOAJ
language English
format Article
sources DOAJ
author Luana Vieira Mukamal
Celso Tavares Sodré
Lara Beatriz Prata
Fernanda Nakasato
Tullia Cuzzi
Marcia Ramos-e-Silva
spellingShingle Luana Vieira Mukamal
Celso Tavares Sodré
Lara Beatriz Prata
Fernanda Nakasato
Tullia Cuzzi
Marcia Ramos-e-Silva
Churg-Strauss Syndrome or Eosinophilic Granulomatosis with Polyangiitis: Exuberant Classic Clinical Picture of a Rare Disease
Case Reports in Dermatology
Churg-Strauss syndrome
Allergic granulomatous angiitis
Vasculitis
author_facet Luana Vieira Mukamal
Celso Tavares Sodré
Lara Beatriz Prata
Fernanda Nakasato
Tullia Cuzzi
Marcia Ramos-e-Silva
author_sort Luana Vieira Mukamal
title Churg-Strauss Syndrome or Eosinophilic Granulomatosis with Polyangiitis: Exuberant Classic Clinical Picture of a Rare Disease
title_short Churg-Strauss Syndrome or Eosinophilic Granulomatosis with Polyangiitis: Exuberant Classic Clinical Picture of a Rare Disease
title_full Churg-Strauss Syndrome or Eosinophilic Granulomatosis with Polyangiitis: Exuberant Classic Clinical Picture of a Rare Disease
title_fullStr Churg-Strauss Syndrome or Eosinophilic Granulomatosis with Polyangiitis: Exuberant Classic Clinical Picture of a Rare Disease
title_full_unstemmed Churg-Strauss Syndrome or Eosinophilic Granulomatosis with Polyangiitis: Exuberant Classic Clinical Picture of a Rare Disease
title_sort churg-strauss syndrome or eosinophilic granulomatosis with polyangiitis: exuberant classic clinical picture of a rare disease
publisher Karger Publishers
series Case Reports in Dermatology
issn 1662-6567
publishDate 2018-06-01
description The authors present a classic case of Churg-Strauss syndrome with an exuberant clinical picture in a 34-year-old woman. She showed the following diagnostic criteria: asthma, polyneuropathy, rhinopathy, marked eosinophilia, positive p-ANCA with a perinuclear pattern, and skin histopathology results suggestive of vasculitis with eosinophils. There was a good response to prednisone, dexamethasone pulse therapy, and cyclophosphamide.
topic Churg-Strauss syndrome
Allergic granulomatous angiitis
Vasculitis
url https://www.karger.com/Article/FullText/489162
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