Primary perforating dermatoses – current status
Primary perforating dermatoses (PPD) are a group of skin diseases rarely seen in everyday dermatological practice, which includes elastosis perforans serpiginosa, reactive perforating collagenosis, Kyrle disease and perforating folliculitis. These entities can be associated with chromosomal aberrati...
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2016-10-01
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doaj-42484c7ba59441c59c3491bb208d0b5a2020-11-24T20:59:36ZengTermedia Publishing HousePrzegląd Dermatologiczny0033-25262084-98932016-10-01103540941610.5114/dr.2016.6289428523Primary perforating dermatoses – current statusKlaudia Orłowska-OrlikAnna WoźniackaJolanta D. TorzeckaPrimary perforating dermatoses (PPD) are a group of skin diseases rarely seen in everyday dermatological practice, which includes elastosis perforans serpiginosa, reactive perforating collagenosis, Kyrle disease and perforating folliculitis. These entities can be associated with chromosomal aberrations, chronic renal, cardiovascular or hepatic diseases. Unique histopathological findings in each PPD are useful in determination of the diagnosis. However, in other more frequently seen dermatoses of heterogeneous etiology, perforation of epidermis with material undergoing transepidermal elimination is also observed. Our article aims to present the most important recent information on epidemiology, pathogenesis, clinical findings, therapeutic options and differential diagnosis of primary perforating dermatoses.https://www.termedia.pl/Primary-perforating-dermatoses-current-status,56,28523,1,1.htmlperforating dermatoses elastosis perforans serpiginosa reactive perforating collagenosis Kyrle disease perforating folliculitis |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Klaudia Orłowska-Orlik Anna Woźniacka Jolanta D. Torzecka |
spellingShingle |
Klaudia Orłowska-Orlik Anna Woźniacka Jolanta D. Torzecka Primary perforating dermatoses – current status Przegląd Dermatologiczny perforating dermatoses elastosis perforans serpiginosa reactive perforating collagenosis Kyrle disease perforating folliculitis |
author_facet |
Klaudia Orłowska-Orlik Anna Woźniacka Jolanta D. Torzecka |
author_sort |
Klaudia Orłowska-Orlik |
title |
Primary perforating dermatoses – current status |
title_short |
Primary perforating dermatoses – current status |
title_full |
Primary perforating dermatoses – current status |
title_fullStr |
Primary perforating dermatoses – current status |
title_full_unstemmed |
Primary perforating dermatoses – current status |
title_sort |
primary perforating dermatoses – current status |
publisher |
Termedia Publishing House |
series |
Przegląd Dermatologiczny |
issn |
0033-2526 2084-9893 |
publishDate |
2016-10-01 |
description |
Primary perforating dermatoses (PPD) are a group of skin diseases rarely seen in everyday dermatological practice, which includes elastosis perforans serpiginosa, reactive perforating collagenosis, Kyrle disease and perforating folliculitis. These entities can be associated with chromosomal aberrations, chronic renal, cardiovascular or hepatic diseases. Unique histopathological findings in each PPD are useful in determination of the diagnosis. However, in other more frequently seen dermatoses of heterogeneous etiology, perforation of epidermis with material undergoing transepidermal elimination is also observed. Our article aims to present the most important recent information on epidemiology, pathogenesis, clinical findings, therapeutic options and differential diagnosis of primary perforating dermatoses. |
topic |
perforating dermatoses elastosis perforans serpiginosa reactive perforating collagenosis Kyrle disease perforating folliculitis |
url |
https://www.termedia.pl/Primary-perforating-dermatoses-current-status,56,28523,1,1.html |
work_keys_str_mv |
AT klaudiaorłowskaorlik primaryperforatingdermatosescurrentstatus AT annawozniacka primaryperforatingdermatosescurrentstatus AT jolantadtorzecka primaryperforatingdermatosescurrentstatus |
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1716782207940427776 |