Severe mononeuritis multiplex in a patient with eosinophilic granulomatosis with polyangiitis
Eosinophilic granulomatosis with polyangiitis (EGPA) is a systemic vasculitis characterised by bronchial asthma, hypereosinophilia, and systemic vasculitis. History of asthma with blood eosinophilia and multiorgan involvement are the important clues to suspect EGPA. In the original paper by Churg an...
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doaj-46668c8fc40446339a8b772a73d195972020-11-25T03:21:30ZengTermedia Publishing HouseRheumatology0034-62332084-98342019-10-0157528829110.5114/reum.2019.8952238508Severe mononeuritis multiplex in a patient with eosinophilic granulomatosis with polyangiitisDesislava KalinovaGeorgi KukushevZlatimir KolarovRasho RashkovEosinophilic granulomatosis with polyangiitis (EGPA) is a systemic vasculitis characterised by bronchial asthma, hypereosinophilia, and systemic vasculitis. History of asthma with blood eosinophilia and multiorgan involvement are the important clues to suspect EGPA. In the original paper by Churg and Strauss cardiac, gastrointestinal tract, renal, and neurological involvement were noted more frequently. The pattern of neurological involvement may be mononeuritis multiplex, and symmetrical and asymmetrical polyneuropathy. Mononeuritis multiplex was present in 78.1% while cranial nerves were involved in only 4.1% of cases. Glucocorticosteroids and immunosuppressants, especially cyclophosphamide, have considerably improved the prognosis and overall survival rates in patients with systemic vasculitis, including eosinophilic granulomatosis with polyangiitis. The authors present a clinical case of eosinophilic granulomatosis with polyangiitis with severe mononeuritis multiplex. The case reflects the successful application of a cyclophosphamide regime as a remission inducer.https://www.termedia.pl/Severe-mononeuritis-multiplex-in-a-patient-with-eosinophilic-granulomatosis-with-polyangiitis,18,38508,1,1.htmleosinophilic granulomatosis with polyangiitis vasculitis mononeuritis multiplex granulomatosis process |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Desislava Kalinova Georgi Kukushev Zlatimir Kolarov Rasho Rashkov |
spellingShingle |
Desislava Kalinova Georgi Kukushev Zlatimir Kolarov Rasho Rashkov Severe mononeuritis multiplex in a patient with eosinophilic granulomatosis with polyangiitis Rheumatology eosinophilic granulomatosis with polyangiitis vasculitis mononeuritis multiplex granulomatosis process |
author_facet |
Desislava Kalinova Georgi Kukushev Zlatimir Kolarov Rasho Rashkov |
author_sort |
Desislava Kalinova |
title |
Severe mononeuritis multiplex in a patient with eosinophilic granulomatosis with polyangiitis |
title_short |
Severe mononeuritis multiplex in a patient with eosinophilic granulomatosis with polyangiitis |
title_full |
Severe mononeuritis multiplex in a patient with eosinophilic granulomatosis with polyangiitis |
title_fullStr |
Severe mononeuritis multiplex in a patient with eosinophilic granulomatosis with polyangiitis |
title_full_unstemmed |
Severe mononeuritis multiplex in a patient with eosinophilic granulomatosis with polyangiitis |
title_sort |
severe mononeuritis multiplex in a patient with eosinophilic granulomatosis with polyangiitis |
publisher |
Termedia Publishing House |
series |
Rheumatology |
issn |
0034-6233 2084-9834 |
publishDate |
2019-10-01 |
description |
Eosinophilic granulomatosis with polyangiitis (EGPA) is a systemic vasculitis characterised by bronchial asthma, hypereosinophilia, and systemic vasculitis. History of asthma with blood eosinophilia and multiorgan involvement are the important clues to suspect EGPA. In the original paper by Churg and Strauss cardiac, gastrointestinal tract, renal, and neurological involvement were noted more frequently. The pattern of neurological involvement may be mononeuritis multiplex, and symmetrical and asymmetrical polyneuropathy. Mononeuritis multiplex was present in 78.1% while cranial nerves were involved in only 4.1% of cases. Glucocorticosteroids and immunosuppressants, especially cyclophosphamide, have considerably improved the prognosis and overall survival rates in patients with systemic vasculitis, including eosinophilic granulomatosis with polyangiitis. The authors present a clinical case of eosinophilic granulomatosis with polyangiitis with severe mononeuritis multiplex. The case reflects the successful application of a cyclophosphamide regime as a remission inducer. |
topic |
eosinophilic granulomatosis with polyangiitis vasculitis mononeuritis multiplex granulomatosis process |
url |
https://www.termedia.pl/Severe-mononeuritis-multiplex-in-a-patient-with-eosinophilic-granulomatosis-with-polyangiitis,18,38508,1,1.html |
work_keys_str_mv |
AT desislavakalinova severemononeuritismultiplexinapatientwitheosinophilicgranulomatosiswithpolyangiitis AT georgikukushev severemononeuritismultiplexinapatientwitheosinophilicgranulomatosiswithpolyangiitis AT zlatimirkolarov severemononeuritismultiplexinapatientwitheosinophilicgranulomatosiswithpolyangiitis AT rashorashkov severemononeuritismultiplexinapatientwitheosinophilicgranulomatosiswithpolyangiitis |
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1724614314187292672 |