Successful Management of Neutropenia in a Patient with CD40 Ligand Deficiency by Immunoglobulin Replacement Therapy
Hyper-IgM syndromes are characterized by profound reduction of serum IgG, IgA, and IgE levels with normal or increased concentrations of serum IgM. CD40 ligand deficiency is X-linked form of the disease, which results in a lack of immunoglobulin class switching from IgM to IgG in B cells. In additio...
Main Authors: | Lida Atarod, Asghar Aghamohammadi, Mostafa Moin, Hiro Kanegane, Nima Rezaei, Kiara Rezaei Kalantari, Ali Akbar Amirzagar, Takishi Futatani, Toshio Miyawaki |
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Format: | Article |
Language: | English |
Published: |
Tehran University of Medical Sciences
2007-03-01
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Series: | Iranian Journal of Allergy, Asthma and Immunology |
Subjects: | |
Online Access: | https://ijaai.tums.ac.ir/index.php/ijaai/article/view/163 |
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