Dermatomyositis-like syndrome in x-linked agammaglobulinemia

Primary immunodeficiencies (PIDs) encompass more than 250 different pathological conditions. X-linked agammaglobulinemia (XLA) has been occasionally associated with cutaneous and muscular manifestations resembling dermatomyositis, often termed dermatomyositis-like syndrome (DLS). This syndrome has b...

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Bibliographic Details
Main Authors: Pedro David Carvalho, Carlos Costa, Marília Rodrigues, Maria João Salvador, José António Pereira da Silva, Armando Malcata
Format: Article
Language:English
Published: Sociedade Portuguesa de Reumatologia 2016-01-01
Series:Acta Reumatológica Portuguesa
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Online Access:http://www.actareumatologica.com/files/article/1091_dermatomyositis_like_syndrome_in_x_linked_agammaglobulinemia_file.pdf

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