Herlyn-Werner-Wunderlich syndrome presented with amenorrhea: A rare urogenital anomaly in females
A 13-year-old prepubertal girl had with primary amenorrhea and severe lower abdominal pain. Pelvic ultrasound showed double uterine cavity and a fluid collection in left uterine cavity with diffuse low level internal echoes, which appeared contiguous with the endocervix. Hymen could not be evaluated...
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doaj-4bf0a94d0aa24d34be6bd0a45eb9c25b2020-11-25T01:33:50ZengPed Urol Case RepPediatric Urology Case Reports2148-29692019-10-016613213610.14534/j-pucr.2019655918204Herlyn-Werner-Wunderlich syndrome presented with amenorrhea: A rare urogenital anomaly in femalesMustafa Ayhan Ekici0Pelin Oyardi1Funda Dagistanli2Omur Albayrak3Caglar Cetin4Department of Gynecology and Obstetrics, Faculty of Medicine, Bolu Abant Izzet Baysal University, Bolu, TurkeyDepartment of Gynecology and Obstetrics, Faculty of Medicine, Bolu Abant Izzet Baysal University, Bolu, TurkeyDepartment of Gynecology and Obstetrics, Faculty of Medicine, Bolu Abant Izzet Baysal University, Bolu, TurkeyDepartment of Gynecology and Obstetrics, Faculty of Medicine, Bolu Abant Izzet Baysal University, Bolu, TurkeyDepartment of Gynecology and Obstetrics, Faculty of Medicine, Bolu Abant Izzet Baysal University, Bolu, TurkeyA 13-year-old prepubertal girl had with primary amenorrhea and severe lower abdominal pain. Pelvic ultrasound showed double uterine cavity and a fluid collection in left uterine cavity with diffuse low level internal echoes, which appeared contiguous with the endocervix. Hymen could not be evaluated because the patient could not be taken to the gynecological table the patient was initially diagnosed as imperforate hymen, gynecologic examination was performed with sedation, and hymen has a normal patency. Magnetic resonance imaging (MRI) revealed two uterus and two cervix, normal right endometrial cavity and 17 mm fluid in the left endometrial cavity and compatible with hematometra. Hematocolpos was observed in the left half of the vagina. There was no left kidney and the right kidney was normal. Based on these findings, the patient was diagnosed as Herlyn-Werner-Wunderlich syndrome and vaginal septum resection was performed as treatment. Evaluation of the genital tract by means of MRI scanning or ultrasonography should be recommended in all girls with known renal abnormalities before the onset of menstruation.http://pediatricurologycasereports.com/ojs/index.php/pucr/article/view/474herlyn-werner-wunderlich syndrome, amenorrhea, renal agenesis, hematometra, uterus didelphis. |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Mustafa Ayhan Ekici Pelin Oyardi Funda Dagistanli Omur Albayrak Caglar Cetin |
spellingShingle |
Mustafa Ayhan Ekici Pelin Oyardi Funda Dagistanli Omur Albayrak Caglar Cetin Herlyn-Werner-Wunderlich syndrome presented with amenorrhea: A rare urogenital anomaly in females Pediatric Urology Case Reports herlyn-werner-wunderlich syndrome, amenorrhea, renal agenesis, hematometra, uterus didelphis. |
author_facet |
Mustafa Ayhan Ekici Pelin Oyardi Funda Dagistanli Omur Albayrak Caglar Cetin |
author_sort |
Mustafa Ayhan Ekici |
title |
Herlyn-Werner-Wunderlich syndrome presented with amenorrhea: A rare urogenital anomaly in females |
title_short |
Herlyn-Werner-Wunderlich syndrome presented with amenorrhea: A rare urogenital anomaly in females |
title_full |
Herlyn-Werner-Wunderlich syndrome presented with amenorrhea: A rare urogenital anomaly in females |
title_fullStr |
Herlyn-Werner-Wunderlich syndrome presented with amenorrhea: A rare urogenital anomaly in females |
title_full_unstemmed |
Herlyn-Werner-Wunderlich syndrome presented with amenorrhea: A rare urogenital anomaly in females |
title_sort |
herlyn-werner-wunderlich syndrome presented with amenorrhea: a rare urogenital anomaly in females |
publisher |
Ped Urol Case Rep |
series |
Pediatric Urology Case Reports |
issn |
2148-2969 |
publishDate |
2019-10-01 |
description |
A 13-year-old prepubertal girl had with primary amenorrhea and severe lower abdominal pain. Pelvic ultrasound showed double uterine cavity and a fluid collection in left uterine cavity with diffuse low level internal echoes, which appeared contiguous with the endocervix. Hymen could not be evaluated because the patient could not be taken to the gynecological table the patient was initially diagnosed as imperforate hymen, gynecologic examination was performed with sedation, and hymen has a normal patency. Magnetic resonance imaging (MRI) revealed two uterus and two cervix, normal right endometrial cavity and 17 mm fluid in the left endometrial cavity and compatible with hematometra. Hematocolpos was observed in the left half of the vagina. There was no left kidney and the right kidney was normal. Based on these findings, the patient was diagnosed as Herlyn-Werner-Wunderlich syndrome and vaginal septum resection was performed as treatment. Evaluation of the genital tract by means of MRI scanning or ultrasonography should be recommended in all girls with known renal abnormalities before the onset of menstruation. |
topic |
herlyn-werner-wunderlich syndrome, amenorrhea, renal agenesis, hematometra, uterus didelphis. |
url |
http://pediatricurologycasereports.com/ojs/index.php/pucr/article/view/474 |
work_keys_str_mv |
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