Presacral Ganglioneuroma: Diagnostic Considerations and Therapeutic Strategy
Presacral ganglioneuroma is an extremely rare tumor of neural crest origin. To the best of our knowledge, less than 20 cases have been reported previously. The present study reports on a presacral ganglioneuroma, 10.5 × 8 × 4 cm in size, that was found incidentally in a 35-year-old man with prior hi...
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doaj-50a2a14afc9c44a1acd95d22d6bdfcdb2020-11-24T21:00:27ZengKarger PublishersCase Reports in Oncology1662-65752013-11-016356156810.1159/000356707356707Presacral Ganglioneuroma: Diagnostic Considerations and Therapeutic StrategyKonstantinos VardasDimitrios ManganasGeorgios PapadimitriouVasileios VougasAthanasios BakalisMaria ChantziaraDimitrios ExarhosSpiros DrakopoulosPresacral ganglioneuroma is an extremely rare tumor of neural crest origin. To the best of our knowledge, less than 20 cases have been reported previously. The present study reports on a presacral ganglioneuroma, 10.5 × 8 × 4 cm in size, that was found incidentally in a 35-year-old man with prior history of diverticulitis. He was admitted to our hospital due to lower left abdominal pain. Abdominal computed tomography and magnetic resonance imaging confirmed the extension of the lesion from the S2 level to the coccyx. The mass had low signal intensity on T1-weighted images and heterogeneous high signal intensity on T2-weighted images with no intraspinal or rectal extension. T2-weighted images demonstrated a compartmentalized solid tumor with cystic components. Complete tumor resection with free surgical margins was achieved using an abdominal approach. The patient remains asymptomatic 2 years after surgery. We emphasize on clinical features, radiologic appearance and surgical treatment of this rare entity. The clinical and pathologic features of previously reported studies are also briefly reviewed.http://www.karger.com/Article/FullText/356707GanglioneuromaPresacral ganglioneuromaRetrorectal tumors |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Konstantinos Vardas Dimitrios Manganas Georgios Papadimitriou Vasileios Vougas Athanasios Bakalis Maria Chantziara Dimitrios Exarhos Spiros Drakopoulos |
spellingShingle |
Konstantinos Vardas Dimitrios Manganas Georgios Papadimitriou Vasileios Vougas Athanasios Bakalis Maria Chantziara Dimitrios Exarhos Spiros Drakopoulos Presacral Ganglioneuroma: Diagnostic Considerations and Therapeutic Strategy Case Reports in Oncology Ganglioneuroma Presacral ganglioneuroma Retrorectal tumors |
author_facet |
Konstantinos Vardas Dimitrios Manganas Georgios Papadimitriou Vasileios Vougas Athanasios Bakalis Maria Chantziara Dimitrios Exarhos Spiros Drakopoulos |
author_sort |
Konstantinos Vardas |
title |
Presacral Ganglioneuroma: Diagnostic Considerations and Therapeutic Strategy |
title_short |
Presacral Ganglioneuroma: Diagnostic Considerations and Therapeutic Strategy |
title_full |
Presacral Ganglioneuroma: Diagnostic Considerations and Therapeutic Strategy |
title_fullStr |
Presacral Ganglioneuroma: Diagnostic Considerations and Therapeutic Strategy |
title_full_unstemmed |
Presacral Ganglioneuroma: Diagnostic Considerations and Therapeutic Strategy |
title_sort |
presacral ganglioneuroma: diagnostic considerations and therapeutic strategy |
publisher |
Karger Publishers |
series |
Case Reports in Oncology |
issn |
1662-6575 |
publishDate |
2013-11-01 |
description |
Presacral ganglioneuroma is an extremely rare tumor of neural crest origin. To the best of our knowledge, less than 20 cases have been reported previously. The present study reports on a presacral ganglioneuroma, 10.5 × 8 × 4 cm in size, that was found incidentally in a 35-year-old man with prior history of diverticulitis. He was admitted to our hospital due to lower left abdominal pain. Abdominal computed tomography and magnetic resonance imaging confirmed the extension of the lesion from the S2 level to the coccyx. The mass had low signal intensity on T1-weighted images and heterogeneous high signal intensity on T2-weighted images with no intraspinal or rectal extension. T2-weighted images demonstrated a compartmentalized solid tumor with cystic components. Complete tumor resection with free surgical margins was achieved using an abdominal approach. The patient remains asymptomatic 2 years after surgery. We emphasize on clinical features, radiologic appearance and surgical treatment of this rare entity. The clinical and pathologic features of previously reported studies are also briefly reviewed. |
topic |
Ganglioneuroma Presacral ganglioneuroma Retrorectal tumors |
url |
http://www.karger.com/Article/FullText/356707 |
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