Sturge Weber Syndrome

Sturge Weber Syndrome

Sturge weber syndrome is a rare sporadic condition of mesodermal phacomatosis, also called encephalotrigeminal angio­matosis (synonyms : fourth phacomatosis or mother spot), is a neurocutaneous disorder with angiomas that involve the leptomeninges (leptomeningeal angiomas) and the skin of the face...

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Bibliographic Details
Main Authors: Kazi Nilufar Moly, S.M. Abu Ahsan, Md. Shafiqul lslam
Format: Article
Language:English
Published: Bangabandhu Sheikh Mujib Medical University 2016-07-01
Series:Bangabandhu Sheikh Mujib Medical University Journal
Subjects:
Angioma
Nevus flammeus
Hemangioma
Phakomatosis
Sturge Weber Syndrome
Online Access:https://www.banglajol.info/index.php/BSMMUJ/article/view/28924
Description
Summary:Sturge weber syndrome is a rare sporadic condition of mesodermal phacomatosis, also called encephalotrigeminal angio­matosis (synonyms : fourth phacomatosis or mother spot), is a neurocutaneous disorder with angiomas that involve the leptomeninges (leptomeningeal angiomas) and the skin of the face (purple colored flat cutaneous haemangiomas ), typically in the ophthalmic (V1) and maxillary (V2) distributions of the trigeminal nerve. The hallmark of sturge weber syndrome is a facial cutaneous venous dilation, also referred to as a nevus flammeus or port wine stain (PWS). Because of the rarity, we report here a one & half year old male child who presented with features of the Sturge Weber Syndrome on both side of face.
ISSN:2074-2908
2224-7750

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