Congenital coronary-pulmonary artery fistula originating from right and left coronary artery

• Main Authors: Ali Kemal Gür, Ahmet Karakurt, Yüksel Kaya
• Format: Article
• Language: English
• Published: Dicle University Medical School 2013-12-01
• Series: Dicle Medical Journal
• Subjects: Dyspnea; double arteriovenous fistula; mitral and tricuspid insufficiency
• Online Access: http://www.diclemedj.org/upload/sayi/29/Dicle%20Med%20J-01720.pdf

Coronary artery fistula (CAF) is a rare congenital anomalywith an incidence of 1 in 50 000 live births. The fistula wasobserved at the right coronary artery in 53%, the left coronaryartery in 42% and both coronary artery in 5% of thecases. Echocardiography examination in a 46 year-oldwoman with the symptoms of chest pain, palpitation anddyspnea revealed a severe mitral valve insufficiency anda moderate to severe tricuspid valve insufficiency. A CAForiginating from the proximal part of the left anterior descendingartery (LAD) and another fistula originating fromosteal part of the right coronary artery (RCA) were detectedby coronary angiography. Both fistulas were draininginto the main pulmonary artery. The coronary artery fistulaclosed under cardiopulmonary by-pass. Mitral insufficiencyoriginated from the posterior leaflet was diagnosedintra-operative exploration, and thereafter it was repairedwith mitral annuloplasty including a quadrangular resectionand use of a 32 No St Jude mitral ring. Tricuspid valvewas repaired with Calangos Ring annuloplasty. Followingsix day hospital stay, the woman was discharged free ofany symptom.Key words: Dyspnea, double arteriovenous fistula, mitral and tricuspid insufficiency