Incontinentia pigmenti: A propósito de un caso.
Incontinentia Pigmenti is a rare X-linked multisystem neuroectodermic disorder with signs and symptoms related mainly to the dermatologic, dental, ocular and central nervous systems, and characterized by death in the majority of male embryos. Affected children do not appear sick, in spite of the ski...
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Universidad Peruana Cayetano Heredia
1995-04-01
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doaj-56d1d52e5241417e812af4fc9b74e2ae2020-11-24T22:30:33ZspaUniversidad Peruana Cayetano HerediaRevista Médica Herediana1729-214X1995-04-0163140144S1018-130X1995000300007Incontinentia pigmenti: A propósito de un caso.Carlos Tori Tori0Enriqueta Villar De Cipriani1Javier Arias Stella2Carmen Avalos3Universidad Peruana Cayetano HerediaUniversidad Peruana Cayetano HerediaUniversidad Peruana Cayetano HerediaCentro Oftalmològico, MirafloresIncontinentia Pigmenti is a rare X-linked multisystem neuroectodermic disorder with signs and symptoms related mainly to the dermatologic, dental, ocular and central nervous systems, and characterized by death in the majority of male embryos. Affected children do not appear sick, in spite of the skin eruption, the peripheral leucocytosis and marked eosinophilia. Most of the cases are reported in caucasians, although there are description in black children, orientals, north central and south american Indians, and in our mestizos. The name of Incontinentia Pigmenti describes the incontinence of the melanin pigment from the basal layer of the epidemermis into the superficial dermis.http://www.scielo.org.pe/scielo.php?script=sci_arttext&pid=S1018-130X1995000300007&lng=en&tlng=enIncontinentia PigmentichildrenmelaninBloch Sulzbergerneuroectodermic |
collection |
DOAJ |
language |
Spanish |
format |
Article |
sources |
DOAJ |
author |
Carlos Tori Tori Enriqueta Villar De Cipriani Javier Arias Stella Carmen Avalos |
spellingShingle |
Carlos Tori Tori Enriqueta Villar De Cipriani Javier Arias Stella Carmen Avalos Incontinentia pigmenti: A propósito de un caso. Revista Médica Herediana Incontinentia Pigmenti children melanin Bloch Sulzberger neuroectodermic |
author_facet |
Carlos Tori Tori Enriqueta Villar De Cipriani Javier Arias Stella Carmen Avalos |
author_sort |
Carlos Tori Tori |
title |
Incontinentia pigmenti: A propósito de un caso. |
title_short |
Incontinentia pigmenti: A propósito de un caso. |
title_full |
Incontinentia pigmenti: A propósito de un caso. |
title_fullStr |
Incontinentia pigmenti: A propósito de un caso. |
title_full_unstemmed |
Incontinentia pigmenti: A propósito de un caso. |
title_sort |
incontinentia pigmenti: a propósito de un caso. |
publisher |
Universidad Peruana Cayetano Heredia |
series |
Revista Médica Herediana |
issn |
1729-214X |
publishDate |
1995-04-01 |
description |
Incontinentia Pigmenti is a rare X-linked multisystem neuroectodermic disorder with signs and symptoms related mainly to the dermatologic, dental, ocular and central nervous systems, and characterized by death in the majority of male embryos. Affected children do not appear sick, in spite of the skin eruption, the peripheral leucocytosis and marked eosinophilia. Most of the cases are reported in caucasians, although there are description in black children, orientals, north central and south american Indians, and in our mestizos. The name of Incontinentia Pigmenti describes the incontinence of the melanin pigment from the basal layer of the epidemermis into the superficial dermis. |
topic |
Incontinentia Pigmenti children melanin Bloch Sulzberger neuroectodermic |
url |
http://www.scielo.org.pe/scielo.php?script=sci_arttext&pid=S1018-130X1995000300007&lng=en&tlng=en |
work_keys_str_mv |
AT carlostoritori incontinentiapigmentiapropositodeuncaso AT enriquetavillardecipriani incontinentiapigmentiapropositodeuncaso AT javierariasstella incontinentiapigmentiapropositodeuncaso AT carmenavalos incontinentiapigmentiapropositodeuncaso |
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