Malignant perivascular epithelioid cell tumor of the uterus
Perivascular epithelioid cell tumors (PEComas) are a rare collection of tumors arising in a wide array of anatomic locations and characterized by a myomelanocytic phenotype. PEComas which occur in non‐classic anatomic distributions are known as perivascular epithelioid cell tumor‐not otherwise speci...
Main Authors: | , , |
---|---|
Format: | Article |
Language: | English |
Published: |
SAGE Publishing
2012-01-01
|
Series: | Rare Tumors |
Subjects: | |
Online Access: | http://www.pagepress.org/journals/index.php/rt/article/view/3833 |
id |
doaj-58031fba56db47879c95e970e0dd093f |
---|---|
record_format |
Article |
spelling |
doaj-58031fba56db47879c95e970e0dd093f2020-11-25T03:28:22ZengSAGE PublishingRare Tumors2036-36052036-36132012-01-0141e14e1410.4081/rt.2012.e14Malignant perivascular epithelioid cell tumor of the uterusAndrew L. FolpeJ.Fernando QuevedoJonathan S. BleekerPerivascular epithelioid cell tumors (PEComas) are a rare collection of tumors arising in a wide array of anatomic locations and characterized by a myomelanocytic phenotype. PEComas which occur in non‐classic anatomic distributions are known as perivascular epithelioid cell tumor‐not otherwise specified (PEComa‐NOS), and one of the most common primary sites for PEComa‐NOS is the uterus. The risk of aggressive behavior of these tumors has been linked to a number of factors evaluable on pathologic review following initial surgical resection. We report a case of PEComa‐NOS of the uterus with multiple high‐risk features, including frank vascular invasion, with no evidence of recurrent disease 18 months following initial surgical resection.http://www.pagepress.org/journals/index.php/rt/article/view/3833perivascular epithelioid cell, PEComa, uterine cancer |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Andrew L. Folpe J.Fernando Quevedo Jonathan S. Bleeker |
spellingShingle |
Andrew L. Folpe J.Fernando Quevedo Jonathan S. Bleeker Malignant perivascular epithelioid cell tumor of the uterus Rare Tumors perivascular epithelioid cell, PEComa, uterine cancer |
author_facet |
Andrew L. Folpe J.Fernando Quevedo Jonathan S. Bleeker |
author_sort |
Andrew L. Folpe |
title |
Malignant perivascular epithelioid cell tumor of the uterus |
title_short |
Malignant perivascular epithelioid cell tumor of the uterus |
title_full |
Malignant perivascular epithelioid cell tumor of the uterus |
title_fullStr |
Malignant perivascular epithelioid cell tumor of the uterus |
title_full_unstemmed |
Malignant perivascular epithelioid cell tumor of the uterus |
title_sort |
malignant perivascular epithelioid cell tumor of the uterus |
publisher |
SAGE Publishing |
series |
Rare Tumors |
issn |
2036-3605 2036-3613 |
publishDate |
2012-01-01 |
description |
Perivascular epithelioid cell tumors (PEComas) are a rare collection of tumors arising in a wide array of anatomic locations and characterized by a myomelanocytic phenotype. PEComas which occur in non‐classic anatomic distributions are known as perivascular epithelioid cell tumor‐not otherwise specified (PEComa‐NOS), and one of the most common primary sites for PEComa‐NOS is the uterus. The risk of aggressive behavior of these tumors has been linked to a number of factors evaluable on pathologic review following initial surgical resection. We report a case of PEComa‐NOS of the uterus with multiple high‐risk features, including frank vascular invasion, with no evidence of recurrent disease 18 months following initial surgical resection. |
topic |
perivascular epithelioid cell, PEComa, uterine cancer |
url |
http://www.pagepress.org/journals/index.php/rt/article/view/3833 |
work_keys_str_mv |
AT andrewlfolpe malignantperivascularepithelioidcelltumoroftheuterus AT jfernandoquevedo malignantperivascularepithelioidcelltumoroftheuterus AT jonathansbleeker malignantperivascularepithelioidcelltumoroftheuterus |
_version_ |
1724584661169995776 |