HIRAYAMA DISEASE. CLINICAL CASE AND A REVIEW OF LITERATURE

HIRAYAMA DISEASE. CLINICAL CASE AND A REVIEW OF LITERATURE

Hirayama disease is a rare neurological disease with unilateral or asymmetric bilateral distal upper limb paresis and muscle atrophy. Here  the authors report a clinical case of patient with weakness of cluster muscles and distal asymmetric upper paraparesis. Taking into consideration complaints, cl...

Full description

Bibliographic Details
Main Authors: E. R. Barantsevich, D. I. Rudenko, O. V. Posokhina, A. A. Yakovlev, R. A. Gapeshin, A. G. Smochilin, E. O. Scherbakova
Format: Article
Language:Russian
Published: Academician I.P. Pavlov First St. Petersburg State Medical University 2017-03-01
Series:Učenye Zapiski Sankt-Peterburgskogo Gosudarstvennogo Medicinskogo Universiteta im. Akad. I.P. Pavlova
Subjects:
hirayama disease
monomelic amyotrophy
magnetic resonance tomography with flexion
electroneuromyo-graphy
Online Access:https://www.sci-notes.ru/jour/article/view/367
Description
Summary:Hirayama disease is a rare neurological disease with unilateral or asymmetric bilateral distal upper limb paresis and muscle atrophy. Here  the authors report a clinical case of patient with weakness of cluster muscles and distal asymmetric upper paraparesis. Taking into consideration complaints, clinical presentation and performed follow-up examination (bloodwork, cervical MRI in neutral position and with flexion, MRI of lower limb muscles and electroneuromyography) the patient was diagnosed with Hirayama disease with asymmetric upper extremities. Also, there is a review of literature with pathogenesis, clinical presentation, diagnostic and treatment approaches to this disease.
ISSN:1607-4181

Similar Items