UP-TO-DATE MANAGEMENT OF LIVER DISEASE AND COMPLICATIONS IN CYSTIC FIBROSIS AND TRANSITION OF ADOLESCENTS FROM PEDIATRIC TO ADULT CARE
<p>Cystic fibrosis (CF) is the most common autosomal recessive lethal hereditary disorder among whites. Survival of patients with CF has progressively improved over the last four decades.</p><p>As life expectancy has been greatly extended, complications like osteopenia and CF-relat...
Main Authors: | , , , , |
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Format: | Article |
Language: | English |
Published: |
Slovenian Medical Association
2015-05-01
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Series: | Zdravniški Vestnik |
Subjects: | |
Online Access: | http://vestnik.szd.si/index.php/ZdravVest/article/view/1228 |
Summary: | <p>Cystic fibrosis (CF) is the most common autosomal recessive lethal hereditary disorder among whites. Survival of patients with CF has progressively improved over the last four decades.</p><p>As life expectancy has been greatly extended, complications like osteopenia and CF-related diabetes mellitus (CFRDM) occur. In our article, a new management of these two complications is described.</p><p>Gastrointestinal tract, exocrine pancreas and liver are also affected in CF.</p><p>Maintaining good nutrition while treating pancreatic insufficiency, treating gastroesophageal reflux disease and treating liver disease are very important issues in the treatment gastrointestinal tract disease in CF.</p><p>As the CF patient population median survival increases, a growing number of adolescents require care in the adult health care system which must be capable of responding appropriately to their needs.</p><p>We present a model of transition from paediatric to adult medical care in our CF center.</p> |
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ISSN: | 1318-0347 1581-0224 |