Successful Outcome and Biliary Drainage in an Infant with Concurrent Alpha-1-Antitrypsin Deficiency and Biliary Atresia
We describe the rare instance of concomitant biliary atresia and alpha-1-antitrypsin deficiency and the first documented successful portoenterostomy in this scenario. The potential for dual pathology must be recognized and underscores that prompt diagnosis of biliary atresia, despite concomitant alp...
Main Authors: | , , |
---|---|
Format: | Article |
Language: | English |
Published: |
Hindawi Limited
2017-01-01
|
Series: | Case Reports in Surgery |
Online Access: | http://dx.doi.org/10.1155/2017/9348461 |
id |
doaj-696773096ba3434ba7d43233a33c50b0 |
---|---|
record_format |
Article |
spelling |
doaj-696773096ba3434ba7d43233a33c50b02020-11-24T23:18:47ZengHindawi LimitedCase Reports in Surgery2090-69002090-69192017-01-01201710.1155/2017/93484619348461Successful Outcome and Biliary Drainage in an Infant with Concurrent Alpha-1-Antitrypsin Deficiency and Biliary AtresiaAndrew W. Wang0Kimberly Newton1Karen Kling2Department of Surgery, Naval Medical Center San Diego, San Diego, CA 92134, USADivision of Pediatric Gastroenterology, Hepatology, and Nutrition, Rady Children’s Hospital, San Diego, CA 92123, USADepartment of Surgery, School of Medicine, University of California San Diego, La Jolla, San Diego, CA 92093, USAWe describe the rare instance of concomitant biliary atresia and alpha-1-antitrypsin deficiency and the first documented successful portoenterostomy in this scenario. The potential for dual pathology must be recognized and underscores that prompt diagnosis of biliary atresia, despite concomitant alpha-1-antitrypsin deficiency, is essential to afford potential longstanding native liver function.http://dx.doi.org/10.1155/2017/9348461 |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Andrew W. Wang Kimberly Newton Karen Kling |
spellingShingle |
Andrew W. Wang Kimberly Newton Karen Kling Successful Outcome and Biliary Drainage in an Infant with Concurrent Alpha-1-Antitrypsin Deficiency and Biliary Atresia Case Reports in Surgery |
author_facet |
Andrew W. Wang Kimberly Newton Karen Kling |
author_sort |
Andrew W. Wang |
title |
Successful Outcome and Biliary Drainage in an Infant with Concurrent Alpha-1-Antitrypsin Deficiency and Biliary Atresia |
title_short |
Successful Outcome and Biliary Drainage in an Infant with Concurrent Alpha-1-Antitrypsin Deficiency and Biliary Atresia |
title_full |
Successful Outcome and Biliary Drainage in an Infant with Concurrent Alpha-1-Antitrypsin Deficiency and Biliary Atresia |
title_fullStr |
Successful Outcome and Biliary Drainage in an Infant with Concurrent Alpha-1-Antitrypsin Deficiency and Biliary Atresia |
title_full_unstemmed |
Successful Outcome and Biliary Drainage in an Infant with Concurrent Alpha-1-Antitrypsin Deficiency and Biliary Atresia |
title_sort |
successful outcome and biliary drainage in an infant with concurrent alpha-1-antitrypsin deficiency and biliary atresia |
publisher |
Hindawi Limited |
series |
Case Reports in Surgery |
issn |
2090-6900 2090-6919 |
publishDate |
2017-01-01 |
description |
We describe the rare instance of concomitant biliary atresia and alpha-1-antitrypsin deficiency and the first documented successful portoenterostomy in this scenario. The potential for dual pathology must be recognized and underscores that prompt diagnosis of biliary atresia, despite concomitant alpha-1-antitrypsin deficiency, is essential to afford potential longstanding native liver function. |
url |
http://dx.doi.org/10.1155/2017/9348461 |
work_keys_str_mv |
AT andrewwwang successfuloutcomeandbiliarydrainageinaninfantwithconcurrentalpha1antitrypsindeficiencyandbiliaryatresia AT kimberlynewton successfuloutcomeandbiliarydrainageinaninfantwithconcurrentalpha1antitrypsindeficiencyandbiliaryatresia AT karenkling successfuloutcomeandbiliarydrainageinaninfantwithconcurrentalpha1antitrypsindeficiencyandbiliaryatresia |
_version_ |
1725580050594529280 |