Successful Outcome and Biliary Drainage in an Infant with Concurrent Alpha-1-Antitrypsin Deficiency and Biliary Atresia

Successful Outcome and Biliary Drainage in an Infant with Concurrent Alpha-1-Antitrypsin Deficiency and Biliary Atresia

We describe the rare instance of concomitant biliary atresia and alpha-1-antitrypsin deficiency and the first documented successful portoenterostomy in this scenario. The potential for dual pathology must be recognized and underscores that prompt diagnosis of biliary atresia, despite concomitant alp...

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Main Authors: Andrew W. Wang, Kimberly Newton, Karen Kling
Format: Article
Language:English
Published: Hindawi Limited 2017-01-01
Series:Case Reports in Surgery
Online Access:http://dx.doi.org/10.1155/2017/9348461
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spelling doaj-696773096ba3434ba7d43233a33c50b02020-11-24T23:18:47ZengHindawi LimitedCase Reports in Surgery2090-69002090-69192017-01-01201710.1155/2017/93484619348461Successful Outcome and Biliary Drainage in an Infant with Concurrent Alpha-1-Antitrypsin Deficiency and Biliary AtresiaAndrew W. Wang0Kimberly Newton1Karen Kling2Department of Surgery, Naval Medical Center San Diego, San Diego, CA 92134, USADivision of Pediatric Gastroenterology, Hepatology, and Nutrition, Rady Children’s Hospital, San Diego, CA 92123, USADepartment of Surgery, School of Medicine, University of California San Diego, La Jolla, San Diego, CA 92093, USAWe describe the rare instance of concomitant biliary atresia and alpha-1-antitrypsin deficiency and the first documented successful portoenterostomy in this scenario. The potential for dual pathology must be recognized and underscores that prompt diagnosis of biliary atresia, despite concomitant alpha-1-antitrypsin deficiency, is essential to afford potential longstanding native liver function.http://dx.doi.org/10.1155/2017/9348461
collection DOAJ
language English
format Article
sources DOAJ
author Andrew W. Wang
Kimberly Newton
Karen Kling
spellingShingle Andrew W. Wang
Kimberly Newton
Karen Kling
Successful Outcome and Biliary Drainage in an Infant with Concurrent Alpha-1-Antitrypsin Deficiency and Biliary Atresia
Case Reports in Surgery
author_facet Andrew W. Wang
Kimberly Newton
Karen Kling
author_sort Andrew W. Wang
title Successful Outcome and Biliary Drainage in an Infant with Concurrent Alpha-1-Antitrypsin Deficiency and Biliary Atresia
title_short Successful Outcome and Biliary Drainage in an Infant with Concurrent Alpha-1-Antitrypsin Deficiency and Biliary Atresia
title_full Successful Outcome and Biliary Drainage in an Infant with Concurrent Alpha-1-Antitrypsin Deficiency and Biliary Atresia
title_fullStr Successful Outcome and Biliary Drainage in an Infant with Concurrent Alpha-1-Antitrypsin Deficiency and Biliary Atresia
title_full_unstemmed Successful Outcome and Biliary Drainage in an Infant with Concurrent Alpha-1-Antitrypsin Deficiency and Biliary Atresia
title_sort successful outcome and biliary drainage in an infant with concurrent alpha-1-antitrypsin deficiency and biliary atresia
publisher Hindawi Limited
series Case Reports in Surgery
issn 2090-6900
2090-6919
publishDate 2017-01-01
description We describe the rare instance of concomitant biliary atresia and alpha-1-antitrypsin deficiency and the first documented successful portoenterostomy in this scenario. The potential for dual pathology must be recognized and underscores that prompt diagnosis of biliary atresia, despite concomitant alpha-1-antitrypsin deficiency, is essential to afford potential longstanding native liver function.
url http://dx.doi.org/10.1155/2017/9348461
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AT karenkling successfuloutcomeandbiliarydrainageinaninfantwithconcurrentalpha1antitrypsindeficiencyandbiliaryatresia
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