Novel diagnostic and therapeutic approaches to pulmonary hypertension due to the unilateral absence of a pulmonary artery
Abstract We report the case of a 64‐year‐old female diagnosed with severe pulmonary hypertension due to the unilateral absence of a pulmonary artery. The four‐dimensional computed tomography scan is a useful modality for revealing detailed anatomical findings for differential diagnoses and surgical...
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Online Access: | https://doi.org/10.1002/ehf2.13459 |
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doaj-754ef1bd0f3b4e7595d80b1b7817b4942021-07-28T18:55:37ZengWileyESC Heart Failure2055-58222021-08-01843427343010.1002/ehf2.13459Novel diagnostic and therapeutic approaches to pulmonary hypertension due to the unilateral absence of a pulmonary arteryYuki Nagamatsu0Ayumi Goda1Junnosuke Ito2Kaori Takeuchi3Hanako Kikuchi4Toshiya Kariyasu5Haruhiko Machida6Takumi Inami7Takashi Kohno8Kyoko Soejima9Toru Satoh10Department of Cardiovascular Medicine Kyorin University Hospital 6‐20‐2 Shinkawa, Mitaka Tokyo 181‐8611 JapanDepartment of Cardiovascular Medicine Kyorin University Hospital 6‐20‐2 Shinkawa, Mitaka Tokyo 181‐8611 JapanDepartment of Cardiovascular Medicine Kyorin University Hospital 6‐20‐2 Shinkawa, Mitaka Tokyo 181‐8611 JapanDepartment of Cardiovascular Medicine Kyorin University Hospital 6‐20‐2 Shinkawa, Mitaka Tokyo 181‐8611 JapanDepartment of Cardiovascular Medicine Kyorin University Hospital 6‐20‐2 Shinkawa, Mitaka Tokyo 181‐8611 JapanDepartment of Radiology Kyorin University Hospital Tokyo JapanDepartment of Radiology Kyorin University Hospital Tokyo JapanDepartment of Cardiovascular Medicine Kyorin University Hospital 6‐20‐2 Shinkawa, Mitaka Tokyo 181‐8611 JapanDepartment of Cardiovascular Medicine Kyorin University Hospital 6‐20‐2 Shinkawa, Mitaka Tokyo 181‐8611 JapanDepartment of Cardiovascular Medicine Kyorin University Hospital 6‐20‐2 Shinkawa, Mitaka Tokyo 181‐8611 JapanDepartment of Cardiovascular Medicine Kyorin University Hospital 6‐20‐2 Shinkawa, Mitaka Tokyo 181‐8611 JapanAbstract We report the case of a 64‐year‐old female diagnosed with severe pulmonary hypertension due to the unilateral absence of a pulmonary artery. The four‐dimensional computed tomography scan is a useful modality for revealing detailed anatomical findings for differential diagnoses and surgical decision‐making. The patient had severe pulmonary hypertension with a mean pulmonary artery pressure (PAP) of 74 mmHg and was treated with triple upfront combination therapy, leading to significant improvement in pulmonary haemodynamics (to 27 mmHg in mean PAP) and functional capacity (WHO functional class, from III to II; 6‐min walk distance, from 211 to 276 m).https://doi.org/10.1002/ehf2.13459Unilateral absence of a pulmonary arteryPulmonary hypertension4D computed tomographyUpfront triple combination therapy |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Yuki Nagamatsu Ayumi Goda Junnosuke Ito Kaori Takeuchi Hanako Kikuchi Toshiya Kariyasu Haruhiko Machida Takumi Inami Takashi Kohno Kyoko Soejima Toru Satoh |
spellingShingle |
Yuki Nagamatsu Ayumi Goda Junnosuke Ito Kaori Takeuchi Hanako Kikuchi Toshiya Kariyasu Haruhiko Machida Takumi Inami Takashi Kohno Kyoko Soejima Toru Satoh Novel diagnostic and therapeutic approaches to pulmonary hypertension due to the unilateral absence of a pulmonary artery ESC Heart Failure Unilateral absence of a pulmonary artery Pulmonary hypertension 4D computed tomography Upfront triple combination therapy |
author_facet |
Yuki Nagamatsu Ayumi Goda Junnosuke Ito Kaori Takeuchi Hanako Kikuchi Toshiya Kariyasu Haruhiko Machida Takumi Inami Takashi Kohno Kyoko Soejima Toru Satoh |
author_sort |
Yuki Nagamatsu |
title |
Novel diagnostic and therapeutic approaches to pulmonary hypertension due to the unilateral absence of a pulmonary artery |
title_short |
Novel diagnostic and therapeutic approaches to pulmonary hypertension due to the unilateral absence of a pulmonary artery |
title_full |
Novel diagnostic and therapeutic approaches to pulmonary hypertension due to the unilateral absence of a pulmonary artery |
title_fullStr |
Novel diagnostic and therapeutic approaches to pulmonary hypertension due to the unilateral absence of a pulmonary artery |
title_full_unstemmed |
Novel diagnostic and therapeutic approaches to pulmonary hypertension due to the unilateral absence of a pulmonary artery |
title_sort |
novel diagnostic and therapeutic approaches to pulmonary hypertension due to the unilateral absence of a pulmonary artery |
publisher |
Wiley |
series |
ESC Heart Failure |
issn |
2055-5822 |
publishDate |
2021-08-01 |
description |
Abstract We report the case of a 64‐year‐old female diagnosed with severe pulmonary hypertension due to the unilateral absence of a pulmonary artery. The four‐dimensional computed tomography scan is a useful modality for revealing detailed anatomical findings for differential diagnoses and surgical decision‐making. The patient had severe pulmonary hypertension with a mean pulmonary artery pressure (PAP) of 74 mmHg and was treated with triple upfront combination therapy, leading to significant improvement in pulmonary haemodynamics (to 27 mmHg in mean PAP) and functional capacity (WHO functional class, from III to II; 6‐min walk distance, from 211 to 276 m). |
topic |
Unilateral absence of a pulmonary artery Pulmonary hypertension 4D computed tomography Upfront triple combination therapy |
url |
https://doi.org/10.1002/ehf2.13459 |
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