Hugh-Stovin syndrome: the ‘incomplete Behcet’s disease’. A case study of a young adult with recurrent pulmonary embolism and pulmonary arterial aneurysms

Hugh-Stovin Syndrome (HSS) is characterized by recurrent thrombophlebitis and multiple pulmonary and/or bronchial artery aneurysms indistinguishable from the cardiovascular features seen in Behcet’s disease (BD). Our case describes a 30-year-old male with recurrent pulmonary embolism and bilateral p...

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Main Authors:	Chinedu Ukemenam, Sivaram Prabhuji Muppaneni, Debapriya De, Alexandre Lacasse
Format:	Article
Language:	English
Published:	Taylor & Francis Group 2021-07-01
Series:	Journal of Community Hospital Internal Medicine Perspectives
Subjects:	hugh-stovin thrombophlebitis pulmonary artery aneurysms vasculitides behcet’s disease
Online Access:	http://dx.doi.org/10.1080/20009666.2020.1816273

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spelling	doaj-7cdc14fbea7540a78bc4b9d69e38dc662021-07-15T13:47:53ZengTaylor & Francis GroupJournal of Community Hospital Internal Medicine Perspectives2000-96662021-07-0111456656710.1080/20009666.2020.18162731816273Hugh-Stovin syndrome: the ‘incomplete Behcet’s disease’. A case study of a young adult with recurrent pulmonary embolism and pulmonary arterial aneurysmsChinedu Ukemenam0Sivaram Prabhuji Muppaneni1Debapriya De2Alexandre Lacasse3SSM Saint Mary’s HospitalSSM Saint Mary’s HospitalSSM Saint Mary’s HospitalSSM Saint Mary’s HospitalHugh-Stovin Syndrome (HSS) is characterized by recurrent thrombophlebitis and multiple pulmonary and/or bronchial artery aneurysms indistinguishable from the cardiovascular features seen in Behcet’s disease (BD). Our case describes a 30-year-old male with recurrent pulmonary embolism and bilateral pulmonary aneurysms. Autoimmune, hypercoagulable, and infectious work up were negative. Elevated inflammatory markers and absence of the typical clinical findings seen in BD led to the diagnosis of Hugh-Stovin syndrome (HSS). Immunosuppression using steroids and azathioprine led to clinical response. Anticoagulation was continued based on risk/benefit ratio.http://dx.doi.org/10.1080/20009666.2020.1816273hugh-stovinthrombophlebitispulmonary artery aneurysmsvasculitidesbehcet’s disease
collection	DOAJ
language	English
format	Article
sources	DOAJ
author	Chinedu Ukemenam Sivaram Prabhuji Muppaneni Debapriya De Alexandre Lacasse
spellingShingle	Chinedu Ukemenam Sivaram Prabhuji Muppaneni Debapriya De Alexandre Lacasse Hugh-Stovin syndrome: the ‘incomplete Behcet’s disease’. A case study of a young adult with recurrent pulmonary embolism and pulmonary arterial aneurysms Journal of Community Hospital Internal Medicine Perspectives hugh-stovin thrombophlebitis pulmonary artery aneurysms vasculitides behcet’s disease
author_facet	Chinedu Ukemenam Sivaram Prabhuji Muppaneni Debapriya De Alexandre Lacasse
author_sort	Chinedu Ukemenam
title	Hugh-Stovin syndrome: the ‘incomplete Behcet’s disease’. A case study of a young adult with recurrent pulmonary embolism and pulmonary arterial aneurysms
title_short	Hugh-Stovin syndrome: the ‘incomplete Behcet’s disease’. A case study of a young adult with recurrent pulmonary embolism and pulmonary arterial aneurysms
title_full	Hugh-Stovin syndrome: the ‘incomplete Behcet’s disease’. A case study of a young adult with recurrent pulmonary embolism and pulmonary arterial aneurysms
title_fullStr	Hugh-Stovin syndrome: the ‘incomplete Behcet’s disease’. A case study of a young adult with recurrent pulmonary embolism and pulmonary arterial aneurysms
title_full_unstemmed	Hugh-Stovin syndrome: the ‘incomplete Behcet’s disease’. A case study of a young adult with recurrent pulmonary embolism and pulmonary arterial aneurysms
title_sort	hugh-stovin syndrome: the ‘incomplete behcet’s disease’. a case study of a young adult with recurrent pulmonary embolism and pulmonary arterial aneurysms
publisher	Taylor & Francis Group
series	Journal of Community Hospital Internal Medicine Perspectives
issn	2000-9666
publishDate	2021-07-01
description	Hugh-Stovin Syndrome (HSS) is characterized by recurrent thrombophlebitis and multiple pulmonary and/or bronchial artery aneurysms indistinguishable from the cardiovascular features seen in Behcet’s disease (BD). Our case describes a 30-year-old male with recurrent pulmonary embolism and bilateral pulmonary aneurysms. Autoimmune, hypercoagulable, and infectious work up were negative. Elevated inflammatory markers and absence of the typical clinical findings seen in BD led to the diagnosis of Hugh-Stovin syndrome (HSS). Immunosuppression using steroids and azathioprine led to clinical response. Anticoagulation was continued based on risk/benefit ratio.
topic	hugh-stovin thrombophlebitis pulmonary artery aneurysms vasculitides behcet’s disease
url	http://dx.doi.org/10.1080/20009666.2020.1816273
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Hugh-Stovin syndrome: the ‘incomplete Behcet’s disease’. A case study of a young adult with recurrent pulmonary embolism and pulmonary arterial aneurysms

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