Amyloidosis cutis dyschromica: A rare dyschromic pigmentary disorder
Primary cutaneous amyloidosis (PCA) is the deposition of amyloid proteins in the skin without systemic involvement. Amyloidosis cutis dyschromica (ACD) is a rare variant of PCA with onset typically in early childhood or at a prepubertal age. It is more common in the Asian and Southeast Asian people....
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Wolters Kluwer Medknow Publications
2019-01-01
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doaj-7f08bc6ebbbc4e04bb21f2fc3adfd69a2020-11-24T21:59:44ZengWolters Kluwer Medknow PublicationsIndian Journal of Dermatopathology and Diagnostic Dermatology2349-60292349-60292019-01-0161454710.4103/ijdpdd.ijdpdd_49_18Amyloidosis cutis dyschromica: A rare dyschromic pigmentary disorderKuldeep VermaReena Kumari SharmaAnchana GulatiMudita GuptaPrimary cutaneous amyloidosis (PCA) is the deposition of amyloid proteins in the skin without systemic involvement. Amyloidosis cutis dyschromica (ACD) is a rare variant of PCA with onset typically in early childhood or at a prepubertal age. It is more common in the Asian and Southeast Asian people. Clinically it manifests as asymptomatic diffuse hyperpigmentation interspersed with hypopigmented spots without papulation. Histologically, small foci of amyloid closely under the epidermis are seen. There are only few case reports in the literature of this rarer variant. We report a case of a 32-year-old male presenting as dyschromatosis with a prepubertal onset and histopathological evidence of intradermal deposits in the upper dermis which was confirmed on Congo red staining and hence was diagnosed as a case of ACD.http://www.ijdpdd.com/article.asp?issn=2349-6029;year=2019;volume=6;issue=1;spage=45;epage=47;aulast=VermaAmyloidosisdyschromatosisgeneralized |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Kuldeep Verma Reena Kumari Sharma Anchana Gulati Mudita Gupta |
spellingShingle |
Kuldeep Verma Reena Kumari Sharma Anchana Gulati Mudita Gupta Amyloidosis cutis dyschromica: A rare dyschromic pigmentary disorder Indian Journal of Dermatopathology and Diagnostic Dermatology Amyloidosis dyschromatosis generalized |
author_facet |
Kuldeep Verma Reena Kumari Sharma Anchana Gulati Mudita Gupta |
author_sort |
Kuldeep Verma |
title |
Amyloidosis cutis dyschromica: A rare dyschromic pigmentary disorder |
title_short |
Amyloidosis cutis dyschromica: A rare dyschromic pigmentary disorder |
title_full |
Amyloidosis cutis dyschromica: A rare dyschromic pigmentary disorder |
title_fullStr |
Amyloidosis cutis dyschromica: A rare dyschromic pigmentary disorder |
title_full_unstemmed |
Amyloidosis cutis dyschromica: A rare dyschromic pigmentary disorder |
title_sort |
amyloidosis cutis dyschromica: a rare dyschromic pigmentary disorder |
publisher |
Wolters Kluwer Medknow Publications |
series |
Indian Journal of Dermatopathology and Diagnostic Dermatology |
issn |
2349-6029 2349-6029 |
publishDate |
2019-01-01 |
description |
Primary cutaneous amyloidosis (PCA) is the deposition of amyloid proteins in the skin without systemic involvement. Amyloidosis cutis dyschromica (ACD) is a rare variant of PCA with onset typically in early childhood or at a prepubertal age. It is more common in the Asian and Southeast Asian people. Clinically it manifests as asymptomatic diffuse hyperpigmentation interspersed with hypopigmented spots without papulation. Histologically, small foci of amyloid closely under the epidermis are seen. There are only few case reports in the literature of this rarer variant. We report a case of a 32-year-old male presenting as dyschromatosis with a prepubertal onset and histopathological evidence of intradermal deposits in the upper dermis which was confirmed on Congo red staining and hence was diagnosed as a case of ACD. |
topic |
Amyloidosis dyschromatosis generalized |
url |
http://www.ijdpdd.com/article.asp?issn=2349-6029;year=2019;volume=6;issue=1;spage=45;epage=47;aulast=Verma |
work_keys_str_mv |
AT kuldeepverma amyloidosiscutisdyschromicaararedyschromicpigmentarydisorder AT reenakumarisharma amyloidosiscutisdyschromicaararedyschromicpigmentarydisorder AT anchanagulati amyloidosiscutisdyschromicaararedyschromicpigmentarydisorder AT muditagupta amyloidosiscutisdyschromicaararedyschromicpigmentarydisorder |
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