Supravalvular Congenital Mitral Stenosis

Congenital supravalvular mitral stenosis is a rare malformation characterized by the presence of a shelf-like fibrous membrane, with 1 or 2 small orifices, covering and obstructing the mitral valve. The membrane is positioned closely to the mitral valve (and sometimes it is attached to it); therefor...

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Bibliographic Details
Main Authors: Fernando Moraes, Cleuza Lapa, Cristina Ventura, Rejane Santana, Euclides Tenório, Claudio Gomes, Carlos R. Moraes
Format: Article
Language:English
Published: Sociedade Brasileira de Cardiologia (SBC) 2002-07-01
Series:Arquivos Brasileiros de Cardiologia
Online Access:http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0066-782X2002001000008
Description
Summary:Congenital supravalvular mitral stenosis is a rare malformation characterized by the presence of a shelf-like fibrous membrane, with 1 or 2 small orifices, covering and obstructing the mitral valve. The membrane is positioned closely to the mitral valve (and sometimes it is attached to it); therefore, a preoperative diagnosis is inevitably difficult, even with the use of biplane echocardiography. Two patients with supravalvular mitral stenosis aged 3 years and 3 months are described. In 1 patient, a preoperative diagnosis was made, and both successfully underwent correction.
ISSN:0066-782X
1678-4170