Linear scleroderma and primary sclerosing cholangitis: An undescribed association

Linear scleroderma and primary sclerosing cholangitis: An undescribed association

Linear scleroderma (LS) is clinically characterized by the presence of sclerotic areas of skin, which develop in a linear pattern. Primary sclerosing cholangitis is a cholestatic disorder that can lead to end-stage liver disease. We present, for the first time in English literature, the case of a pa...

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Bibliographic Details
Main Authors: Iñigo Navarro Fernández, Susana Armesto Alonso, Carlos Duran Vian, L Reguero Del Cura, Carmen González-Vela, Marcos González-López
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2020-01-01
Series:Indian Journal of Dermatology
Subjects:
linear scleroderma
morphea
primary sclerosing cholangitis
Online Access:http://www.e-ijd.org/article.asp?issn=0019-5154;year=2020;volume=65;issue=6;spage=514;epage=515;aulast=Fernández
Description
Summary:Linear scleroderma (LS) is clinically characterized by the presence of sclerotic areas of skin, which develop in a linear pattern. Primary sclerosing cholangitis is a cholestatic disorder that can lead to end-stage liver disease. We present, for the first time in English literature, the case of a patient suffering from both the diseases. This highlights the fact that, even though LS has conventionally been considered to be a form of localized scleroderma, this does not necessarily imply that it is an exclusively cutaneous disease.
ISSN:0019-5154
1998-3611

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