The importance of the otorhinolaryngologic evaluation in mucopolysaccharidosis patients

The importance of the otorhinolaryngologic evaluation in mucopolysaccharidosis patients

Introduction: Mucopolysaccharidosis (MPS) is a group of rare diseases caused by the deficit of lysosomal enzymes, causing an accumulation of glycosaminoglycans (GAG) in organs and tissues responsible for the multi-systemic clinical, chronic and progressive status. Objective: Describe the profile of...

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Bibliographic Details
Main Authors:	Bicalho, Cibele Gomes, Rezende, Morena Morais, Nogueira, Ana Maria Carrilho Moinhos, Paulon, Roberta Melo Calvoso, Acosta, Angelina Xavier
Format:	Article
Language:	English
Published:	Thieme Revinter Publicações Ltda. 2011-07-01
Series:	International Archives of Otorhinolaryngology
Subjects:	glycosaminoglycans mucopolysaccharidosis otolaryngology.
Online Access:	http://www.internationalarchivesent.org/conteudo/acervo_eng.asp?id=780

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