Leukocytoclastic Vasculitis as an Extraintestinal Manifestation of Crohn’s Disease
Cutaneous involvement is one of the most common extraintestinal manifestations of inflammatory bowel disease (IBD). More commonly, pyoderma gangrenosum and erythema nodosum are noted, but psoriasis, aphthous stomatitis, Sweet’s syndrome, and vasculitis may also occur. Leukocytoclastic vasculitis (LC...
Main Authors: | , , , , , , , , , |
---|---|
Format: | Article |
Language: | English |
Published: |
Karger Publishers
2021-09-01
|
Series: | Case Reports in Gastroenterology |
Subjects: | |
Online Access: | https://www.karger.com/Article/FullText/519003 |
id |
doaj-86bdd54640fc40238c09d88679110f97 |
---|---|
record_format |
Article |
spelling |
doaj-86bdd54640fc40238c09d88679110f972021-10-07T13:44:27ZengKarger PublishersCase Reports in Gastroenterology1662-06312021-09-0115382583110.1159/000519003519003Leukocytoclastic Vasculitis as an Extraintestinal Manifestation of Crohn’s DiseaseThiara Barcelos Rocha0Ana Lorena Sousa de Vasconcelos Garate1Rodrigo Fedatto Beraldo2Sean Hideo Shirata Lanças3Fábio Vicente Leite4Rodrigo Quera5Jaqueline Ribeiro Barros6Julio Pinheiro Baima7Rogerio Saad-Hossne8Ligia Yukie Sassaki9https://orcid.org/0000-0002-7319-8906São Paulo State University (Unesp), Medical School, Botucatu, BrazilSão Paulo State University (Unesp), Medical School, Botucatu, BrazilSão Paulo State University (Unesp), Medical School, Botucatu, BrazilSão Paulo State University (Unesp), Medical School, Botucatu, BrazilSão Paulo State University (Unesp), Medical School, Botucatu, BrazilClinica Universidad de los Andes, Santiago, ChileSão Paulo State University (Unesp), Medical School, Botucatu, BrazilSão Paulo State University (Unesp), Medical School, Botucatu, BrazilSão Paulo State University (Unesp), Medical School, Botucatu, BrazilSão Paulo State University (Unesp), Medical School, Botucatu, BrazilCutaneous involvement is one of the most common extraintestinal manifestations of inflammatory bowel disease (IBD). More commonly, pyoderma gangrenosum and erythema nodosum are noted, but psoriasis, aphthous stomatitis, Sweet’s syndrome, and vasculitis may also occur. Leukocytoclastic vasculitis (LCV) is a rare cutaneous manifestation, characterized by the appearance of palpable purpura, urticaria, and ulcer-necrotic lesions predominantly in the lower extremities that improve with immunosuppressive therapy. In this case, we report a patient with CD and LCV. We also searched the literature on the diagnosis and treatment of LCV in patients with CD. Female, 31, presented with diarrhea containing mucus and blood, abdominal pain, arthralgia, and enanthematous plaques and ulcers with a hematinic background in the lower extremities. The results of the colonoscopy were compatible with CD and skin biopsy showed signs of LCV. Systemic autoimmune disease and primary vasculitis were ruled out. The patient received treatment with a systemic corticosteroid and the skin lesions improved. Outpatient treatment with antitumor necrosis factor therapy was initiated to promote skin healing and IBD clinical remission. As LCV is a rare manifestation of IBD, it is necessary to distinguish this dermatopathy from other systemic vasculitis. The engagement of a multidisciplinary team is essential for the correct diagnosis and management.https://www.karger.com/Article/FullText/519003leukocytoclastic vasculitisextraintestinal manifestationcrohn’s diseaseinflammatory bowel diseasecase report |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Thiara Barcelos Rocha Ana Lorena Sousa de Vasconcelos Garate Rodrigo Fedatto Beraldo Sean Hideo Shirata Lanças Fábio Vicente Leite Rodrigo Quera Jaqueline Ribeiro Barros Julio Pinheiro Baima Rogerio Saad-Hossne Ligia Yukie Sassaki |
spellingShingle |
Thiara Barcelos Rocha Ana Lorena Sousa de Vasconcelos Garate Rodrigo Fedatto Beraldo Sean Hideo Shirata Lanças Fábio Vicente Leite Rodrigo Quera Jaqueline Ribeiro Barros Julio Pinheiro Baima Rogerio Saad-Hossne Ligia Yukie Sassaki Leukocytoclastic Vasculitis as an Extraintestinal Manifestation of Crohn’s Disease Case Reports in Gastroenterology leukocytoclastic vasculitis extraintestinal manifestation crohn’s disease inflammatory bowel disease case report |
author_facet |
Thiara Barcelos Rocha Ana Lorena Sousa de Vasconcelos Garate Rodrigo Fedatto Beraldo Sean Hideo Shirata Lanças Fábio Vicente Leite Rodrigo Quera Jaqueline Ribeiro Barros Julio Pinheiro Baima Rogerio Saad-Hossne Ligia Yukie Sassaki |
author_sort |
Thiara Barcelos Rocha |
title |
Leukocytoclastic Vasculitis as an Extraintestinal Manifestation of Crohn’s Disease |
title_short |
Leukocytoclastic Vasculitis as an Extraintestinal Manifestation of Crohn’s Disease |
title_full |
Leukocytoclastic Vasculitis as an Extraintestinal Manifestation of Crohn’s Disease |
title_fullStr |
Leukocytoclastic Vasculitis as an Extraintestinal Manifestation of Crohn’s Disease |
title_full_unstemmed |
Leukocytoclastic Vasculitis as an Extraintestinal Manifestation of Crohn’s Disease |
title_sort |
leukocytoclastic vasculitis as an extraintestinal manifestation of crohn’s disease |
publisher |
Karger Publishers |
series |
Case Reports in Gastroenterology |
issn |
1662-0631 |
publishDate |
2021-09-01 |
description |
Cutaneous involvement is one of the most common extraintestinal manifestations of inflammatory bowel disease (IBD). More commonly, pyoderma gangrenosum and erythema nodosum are noted, but psoriasis, aphthous stomatitis, Sweet’s syndrome, and vasculitis may also occur. Leukocytoclastic vasculitis (LCV) is a rare cutaneous manifestation, characterized by the appearance of palpable purpura, urticaria, and ulcer-necrotic lesions predominantly in the lower extremities that improve with immunosuppressive therapy. In this case, we report a patient with CD and LCV. We also searched the literature on the diagnosis and treatment of LCV in patients with CD. Female, 31, presented with diarrhea containing mucus and blood, abdominal pain, arthralgia, and enanthematous plaques and ulcers with a hematinic background in the lower extremities. The results of the colonoscopy were compatible with CD and skin biopsy showed signs of LCV. Systemic autoimmune disease and primary vasculitis were ruled out. The patient received treatment with a systemic corticosteroid and the skin lesions improved. Outpatient treatment with antitumor necrosis factor therapy was initiated to promote skin healing and IBD clinical remission. As LCV is a rare manifestation of IBD, it is necessary to distinguish this dermatopathy from other systemic vasculitis. The engagement of a multidisciplinary team is essential for the correct diagnosis and management. |
topic |
leukocytoclastic vasculitis extraintestinal manifestation crohn’s disease inflammatory bowel disease case report |
url |
https://www.karger.com/Article/FullText/519003 |
work_keys_str_mv |
AT thiarabarcelosrocha leukocytoclasticvasculitisasanextraintestinalmanifestationofcrohnsdisease AT analorenasousadevasconcelosgarate leukocytoclasticvasculitisasanextraintestinalmanifestationofcrohnsdisease AT rodrigofedattoberaldo leukocytoclasticvasculitisasanextraintestinalmanifestationofcrohnsdisease AT seanhideoshiratalancas leukocytoclasticvasculitisasanextraintestinalmanifestationofcrohnsdisease AT fabiovicenteleite leukocytoclasticvasculitisasanextraintestinalmanifestationofcrohnsdisease AT rodrigoquera leukocytoclasticvasculitisasanextraintestinalmanifestationofcrohnsdisease AT jaquelineribeirobarros leukocytoclasticvasculitisasanextraintestinalmanifestationofcrohnsdisease AT juliopinheirobaima leukocytoclasticvasculitisasanextraintestinalmanifestationofcrohnsdisease AT rogeriosaadhossne leukocytoclasticvasculitisasanextraintestinalmanifestationofcrohnsdisease AT ligiayukiesassaki leukocytoclasticvasculitisasanextraintestinalmanifestationofcrohnsdisease |
_version_ |
1716839333443403776 |