Eosinophilic granulomatosis with polyangiitis (formerly known as Churg-Strauss syndrome) as a differential diagnosis of hypereosinophilic syndromes
Eosinophilic granulomatosis with polyangiitis (EGPA), formerly known as Churg-Strauss syndrome, is a rare systemic disease situated between primary small vessel vasculitides associated with antineutrophil cytoplasmic antibodies (ANCAs) and hypereosinophilic syndromes (HES). Here, we present a case o...
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doaj-8a7f5585cbd24c5c82414ea5906c986d2020-11-25T01:06:39ZengElsevierRespiratory Medicine Case Reports2213-00712017-01-0121C1610.1016/j.rmcr.2017.03.006Eosinophilic granulomatosis with polyangiitis (formerly known as Churg-Strauss syndrome) as a differential diagnosis of hypereosinophilic syndromesYuri Albuquerque Pessoa Santos0Bruno Rangel Antunes Silva1Pollyanna Natividade Zanconato Barros Assis Lira2Luiz Carlos Aguiar Vaz3Thiago Thomaz Mafort4Leonardo Palermo Bruno5Agnaldo José Lopes6Department of Clinical Medicine, University Hospital Pedro Ernesto, State University of Rio de Janeiro, Boulevard 28 de Setembro, 77, 3º andar, Vila Isabel, 20551-030, Rio de Janeiro, BrazilDepartment of Pneumology, University Hospital Pedro Ernesto, State University of Rio de Janeiro, Boulevard 28 de Setembro, 77, 2º andar, Vila Isabel, 20551-030, Rio de Janeiro, BrazilDepartment of Anatomic Pathology, School of Medical Sciences, State University of Rio de Janeiro, Av. Prof. Manoel de Abreu, 444, 3º andar, Vila Isabel, 20550-170, Rio de Janeiro, BrazilDepartment of Anatomic Pathology, School of Medical Sciences, State University of Rio de Janeiro, Av. Prof. Manoel de Abreu, 444, 3º andar, Vila Isabel, 20550-170, Rio de Janeiro, BrazilDepartment of Pneumology, University Hospital Pedro Ernesto, State University of Rio de Janeiro, Boulevard 28 de Setembro, 77, 2º andar, Vila Isabel, 20551-030, Rio de Janeiro, BrazilDepartment of Pneumology, University Hospital Pedro Ernesto, State University of Rio de Janeiro, Boulevard 28 de Setembro, 77, 2º andar, Vila Isabel, 20551-030, Rio de Janeiro, BrazilDepartment of Pneumology, University Hospital Pedro Ernesto, State University of Rio de Janeiro, Boulevard 28 de Setembro, 77, 2º andar, Vila Isabel, 20551-030, Rio de Janeiro, BrazilEosinophilic granulomatosis with polyangiitis (EGPA), formerly known as Churg-Strauss syndrome, is a rare systemic disease situated between primary small vessel vasculitides associated with antineutrophil cytoplasmic antibodies (ANCAs) and hypereosinophilic syndromes (HES). Here, we present a case of EGPA in a 38-year-old male, with a previous diagnosis of asthma, who presented with fever, migratory lung infiltrates and systemic eosinophilia that was refractory to previous courses of antibiotics. This case highlights the importance of the primary care physician understanding the differential diagnosis of pulmonary eosinophilic syndromes.http://www.sciencedirect.com/science/article/pii/S2213007117300503Eosinophilic granulomatosis with polyangiitisVasculitisHypereosinophilic syndromesEosinophilia |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Yuri Albuquerque Pessoa Santos Bruno Rangel Antunes Silva Pollyanna Natividade Zanconato Barros Assis Lira Luiz Carlos Aguiar Vaz Thiago Thomaz Mafort Leonardo Palermo Bruno Agnaldo José Lopes |
spellingShingle |
Yuri Albuquerque Pessoa Santos Bruno Rangel Antunes Silva Pollyanna Natividade Zanconato Barros Assis Lira Luiz Carlos Aguiar Vaz Thiago Thomaz Mafort Leonardo Palermo Bruno Agnaldo José Lopes Eosinophilic granulomatosis with polyangiitis (formerly known as Churg-Strauss syndrome) as a differential diagnosis of hypereosinophilic syndromes Respiratory Medicine Case Reports Eosinophilic granulomatosis with polyangiitis Vasculitis Hypereosinophilic syndromes Eosinophilia |
author_facet |
Yuri Albuquerque Pessoa Santos Bruno Rangel Antunes Silva Pollyanna Natividade Zanconato Barros Assis Lira Luiz Carlos Aguiar Vaz Thiago Thomaz Mafort Leonardo Palermo Bruno Agnaldo José Lopes |
author_sort |
Yuri Albuquerque Pessoa Santos |
title |
Eosinophilic granulomatosis with polyangiitis (formerly known as Churg-Strauss syndrome) as a differential diagnosis of hypereosinophilic syndromes |
title_short |
Eosinophilic granulomatosis with polyangiitis (formerly known as Churg-Strauss syndrome) as a differential diagnosis of hypereosinophilic syndromes |
title_full |
Eosinophilic granulomatosis with polyangiitis (formerly known as Churg-Strauss syndrome) as a differential diagnosis of hypereosinophilic syndromes |
title_fullStr |
Eosinophilic granulomatosis with polyangiitis (formerly known as Churg-Strauss syndrome) as a differential diagnosis of hypereosinophilic syndromes |
title_full_unstemmed |
Eosinophilic granulomatosis with polyangiitis (formerly known as Churg-Strauss syndrome) as a differential diagnosis of hypereosinophilic syndromes |
title_sort |
eosinophilic granulomatosis with polyangiitis (formerly known as churg-strauss syndrome) as a differential diagnosis of hypereosinophilic syndromes |
publisher |
Elsevier |
series |
Respiratory Medicine Case Reports |
issn |
2213-0071 |
publishDate |
2017-01-01 |
description |
Eosinophilic granulomatosis with polyangiitis (EGPA), formerly known as Churg-Strauss syndrome, is a rare systemic disease situated between primary small vessel vasculitides associated with antineutrophil cytoplasmic antibodies (ANCAs) and hypereosinophilic syndromes (HES). Here, we present a case of EGPA in a 38-year-old male, with a previous diagnosis of asthma, who presented with fever, migratory lung infiltrates and systemic eosinophilia that was refractory to previous courses of antibiotics. This case highlights the importance of the primary care physician understanding the differential diagnosis of pulmonary eosinophilic syndromes. |
topic |
Eosinophilic granulomatosis with polyangiitis Vasculitis Hypereosinophilic syndromes Eosinophilia |
url |
http://www.sciencedirect.com/science/article/pii/S2213007117300503 |
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