Eosinophilic granulomatosis with polyangiitis (formerly known as Churg-Strauss syndrome) as a differential diagnosis of hypereosinophilic syndromes

Eosinophilic granulomatosis with polyangiitis (EGPA), formerly known as Churg-Strauss syndrome, is a rare systemic disease situated between primary small vessel vasculitides associated with antineutrophil cytoplasmic antibodies (ANCAs) and hypereosinophilic syndromes (HES). Here, we present a case o...

Full description

Bibliographic Details
Main Authors: Yuri Albuquerque Pessoa Santos, Bruno Rangel Antunes Silva, Pollyanna Natividade Zanconato Barros Assis Lira, Luiz Carlos Aguiar Vaz, Thiago Thomaz Mafort, Leonardo Palermo Bruno, Agnaldo José Lopes
Format: Article
Language:English
Published: Elsevier 2017-01-01
Series:Respiratory Medicine Case Reports
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2213007117300503
id doaj-8a7f5585cbd24c5c82414ea5906c986d
record_format Article
spelling doaj-8a7f5585cbd24c5c82414ea5906c986d2020-11-25T01:06:39ZengElsevierRespiratory Medicine Case Reports2213-00712017-01-0121C1610.1016/j.rmcr.2017.03.006Eosinophilic granulomatosis with polyangiitis (formerly known as Churg-Strauss syndrome) as a differential diagnosis of hypereosinophilic syndromesYuri Albuquerque Pessoa Santos0Bruno Rangel Antunes Silva1Pollyanna Natividade Zanconato Barros Assis Lira2Luiz Carlos Aguiar Vaz3Thiago Thomaz Mafort4Leonardo Palermo Bruno5Agnaldo José Lopes6Department of Clinical Medicine, University Hospital Pedro Ernesto, State University of Rio de Janeiro, Boulevard 28 de Setembro, 77, 3º andar, Vila Isabel, 20551-030, Rio de Janeiro, BrazilDepartment of Pneumology, University Hospital Pedro Ernesto, State University of Rio de Janeiro, Boulevard 28 de Setembro, 77, 2º andar, Vila Isabel, 20551-030, Rio de Janeiro, BrazilDepartment of Anatomic Pathology, School of Medical Sciences, State University of Rio de Janeiro, Av. Prof. Manoel de Abreu, 444, 3º andar, Vila Isabel, 20550-170, Rio de Janeiro, BrazilDepartment of Anatomic Pathology, School of Medical Sciences, State University of Rio de Janeiro, Av. Prof. Manoel de Abreu, 444, 3º andar, Vila Isabel, 20550-170, Rio de Janeiro, BrazilDepartment of Pneumology, University Hospital Pedro Ernesto, State University of Rio de Janeiro, Boulevard 28 de Setembro, 77, 2º andar, Vila Isabel, 20551-030, Rio de Janeiro, BrazilDepartment of Pneumology, University Hospital Pedro Ernesto, State University of Rio de Janeiro, Boulevard 28 de Setembro, 77, 2º andar, Vila Isabel, 20551-030, Rio de Janeiro, BrazilDepartment of Pneumology, University Hospital Pedro Ernesto, State University of Rio de Janeiro, Boulevard 28 de Setembro, 77, 2º andar, Vila Isabel, 20551-030, Rio de Janeiro, BrazilEosinophilic granulomatosis with polyangiitis (EGPA), formerly known as Churg-Strauss syndrome, is a rare systemic disease situated between primary small vessel vasculitides associated with antineutrophil cytoplasmic antibodies (ANCAs) and hypereosinophilic syndromes (HES). Here, we present a case of EGPA in a 38-year-old male, with a previous diagnosis of asthma, who presented with fever, migratory lung infiltrates and systemic eosinophilia that was refractory to previous courses of antibiotics. This case highlights the importance of the primary care physician understanding the differential diagnosis of pulmonary eosinophilic syndromes.http://www.sciencedirect.com/science/article/pii/S2213007117300503Eosinophilic granulomatosis with polyangiitisVasculitisHypereosinophilic syndromesEosinophilia
collection DOAJ
language English
format Article
sources DOAJ
author Yuri Albuquerque Pessoa Santos
Bruno Rangel Antunes Silva
Pollyanna Natividade Zanconato Barros Assis Lira
Luiz Carlos Aguiar Vaz
Thiago Thomaz Mafort
Leonardo Palermo Bruno
Agnaldo José Lopes
spellingShingle Yuri Albuquerque Pessoa Santos
Bruno Rangel Antunes Silva
Pollyanna Natividade Zanconato Barros Assis Lira
Luiz Carlos Aguiar Vaz
Thiago Thomaz Mafort
Leonardo Palermo Bruno
Agnaldo José Lopes
Eosinophilic granulomatosis with polyangiitis (formerly known as Churg-Strauss syndrome) as a differential diagnosis of hypereosinophilic syndromes
Respiratory Medicine Case Reports
Eosinophilic granulomatosis with polyangiitis
Vasculitis
Hypereosinophilic syndromes
Eosinophilia
author_facet Yuri Albuquerque Pessoa Santos
Bruno Rangel Antunes Silva
Pollyanna Natividade Zanconato Barros Assis Lira
Luiz Carlos Aguiar Vaz
Thiago Thomaz Mafort
Leonardo Palermo Bruno
Agnaldo José Lopes
author_sort Yuri Albuquerque Pessoa Santos
title Eosinophilic granulomatosis with polyangiitis (formerly known as Churg-Strauss syndrome) as a differential diagnosis of hypereosinophilic syndromes
title_short Eosinophilic granulomatosis with polyangiitis (formerly known as Churg-Strauss syndrome) as a differential diagnosis of hypereosinophilic syndromes
title_full Eosinophilic granulomatosis with polyangiitis (formerly known as Churg-Strauss syndrome) as a differential diagnosis of hypereosinophilic syndromes
title_fullStr Eosinophilic granulomatosis with polyangiitis (formerly known as Churg-Strauss syndrome) as a differential diagnosis of hypereosinophilic syndromes
title_full_unstemmed Eosinophilic granulomatosis with polyangiitis (formerly known as Churg-Strauss syndrome) as a differential diagnosis of hypereosinophilic syndromes
title_sort eosinophilic granulomatosis with polyangiitis (formerly known as churg-strauss syndrome) as a differential diagnosis of hypereosinophilic syndromes
publisher Elsevier
series Respiratory Medicine Case Reports
issn 2213-0071
publishDate 2017-01-01
description Eosinophilic granulomatosis with polyangiitis (EGPA), formerly known as Churg-Strauss syndrome, is a rare systemic disease situated between primary small vessel vasculitides associated with antineutrophil cytoplasmic antibodies (ANCAs) and hypereosinophilic syndromes (HES). Here, we present a case of EGPA in a 38-year-old male, with a previous diagnosis of asthma, who presented with fever, migratory lung infiltrates and systemic eosinophilia that was refractory to previous courses of antibiotics. This case highlights the importance of the primary care physician understanding the differential diagnosis of pulmonary eosinophilic syndromes.
topic Eosinophilic granulomatosis with polyangiitis
Vasculitis
Hypereosinophilic syndromes
Eosinophilia
url http://www.sciencedirect.com/science/article/pii/S2213007117300503
work_keys_str_mv AT yurialbuquerquepessoasantos eosinophilicgranulomatosiswithpolyangiitisformerlyknownaschurgstrausssyndromeasadifferentialdiagnosisofhypereosinophilicsyndromes
AT brunorangelantunessilva eosinophilicgranulomatosiswithpolyangiitisformerlyknownaschurgstrausssyndromeasadifferentialdiagnosisofhypereosinophilicsyndromes
AT pollyannanatividadezanconatobarrosassislira eosinophilicgranulomatosiswithpolyangiitisformerlyknownaschurgstrausssyndromeasadifferentialdiagnosisofhypereosinophilicsyndromes
AT luizcarlosaguiarvaz eosinophilicgranulomatosiswithpolyangiitisformerlyknownaschurgstrausssyndromeasadifferentialdiagnosisofhypereosinophilicsyndromes
AT thiagothomazmafort eosinophilicgranulomatosiswithpolyangiitisformerlyknownaschurgstrausssyndromeasadifferentialdiagnosisofhypereosinophilicsyndromes
AT leonardopalermobruno eosinophilicgranulomatosiswithpolyangiitisformerlyknownaschurgstrausssyndromeasadifferentialdiagnosisofhypereosinophilicsyndromes
AT agnaldojoselopes eosinophilicgranulomatosiswithpolyangiitisformerlyknownaschurgstrausssyndromeasadifferentialdiagnosisofhypereosinophilicsyndromes
_version_ 1725188917665202176