Macrophage Activation Syndrome as Initial Presentation of Systemic Lupus Erythematosus
Macrophage activation syndrome (MAS) is known to be a severe and potentially life-threatening complication of rheumatic disorder, especially systemic juvenile rheumatoid arthritis. It is very rare for MAS to be an initial presentation of systemic lupus erythematosus (SLE). Here, we report a 14-year-...
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2008-04-01
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doaj-8c627d6fd00940189a7b27706d13a77d2020-11-24T22:57:45ZengElsevierPediatrics and Neonatology1875-95722008-04-01492394210.1016/S1875-9572(08)60010-8Macrophage Activation Syndrome as Initial Presentation of Systemic Lupus ErythematosusSay-Tin YeapJiunn-Ming SheenHo-Chang KuoKao-Pin HwangKuender D. YangHong-Ren YuMacrophage activation syndrome (MAS) is known to be a severe and potentially life-threatening complication of rheumatic disorder, especially systemic juvenile rheumatoid arthritis. It is very rare for MAS to be an initial presentation of systemic lupus erythematosus (SLE). Here, we report a 14-year-old girl in whom MAS developed as an initial presentation of SLE. With early diagnosis and administration of cyclosporine A, she had a fair outcome. Further testing showed positive anti-dsDNA about 8 months later.http://www.sciencedirect.com/science/article/pii/S1875957208600108cyclosporine Amacrophage activation syndromesystemic lupus erythematosustype V hyperlipo-proteinemia |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Say-Tin Yeap Jiunn-Ming Sheen Ho-Chang Kuo Kao-Pin Hwang Kuender D. Yang Hong-Ren Yu |
spellingShingle |
Say-Tin Yeap Jiunn-Ming Sheen Ho-Chang Kuo Kao-Pin Hwang Kuender D. Yang Hong-Ren Yu Macrophage Activation Syndrome as Initial Presentation of Systemic Lupus Erythematosus Pediatrics and Neonatology cyclosporine A macrophage activation syndrome systemic lupus erythematosus type V hyperlipo-proteinemia |
author_facet |
Say-Tin Yeap Jiunn-Ming Sheen Ho-Chang Kuo Kao-Pin Hwang Kuender D. Yang Hong-Ren Yu |
author_sort |
Say-Tin Yeap |
title |
Macrophage Activation Syndrome as Initial Presentation of Systemic Lupus Erythematosus |
title_short |
Macrophage Activation Syndrome as Initial Presentation of Systemic Lupus Erythematosus |
title_full |
Macrophage Activation Syndrome as Initial Presentation of Systemic Lupus Erythematosus |
title_fullStr |
Macrophage Activation Syndrome as Initial Presentation of Systemic Lupus Erythematosus |
title_full_unstemmed |
Macrophage Activation Syndrome as Initial Presentation of Systemic Lupus Erythematosus |
title_sort |
macrophage activation syndrome as initial presentation of systemic lupus erythematosus |
publisher |
Elsevier |
series |
Pediatrics and Neonatology |
issn |
1875-9572 |
publishDate |
2008-04-01 |
description |
Macrophage activation syndrome (MAS) is known to be a severe and potentially life-threatening complication of rheumatic disorder, especially systemic juvenile rheumatoid arthritis. It is very rare for MAS to be an initial presentation of systemic lupus erythematosus (SLE). Here, we report a 14-year-old girl in whom MAS developed as an initial presentation of SLE. With early diagnosis and administration of cyclosporine A, she had a fair outcome. Further testing showed positive anti-dsDNA about 8 months later. |
topic |
cyclosporine A macrophage activation syndrome systemic lupus erythematosus type V hyperlipo-proteinemia |
url |
http://www.sciencedirect.com/science/article/pii/S1875957208600108 |
work_keys_str_mv |
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1725649327533064192 |