A Rare Cause of Abdominal Pain in Children: Hereditary Angioedema

Hereditary angioedema (HA) is a rare, autosomal-dominant genetic disorder presenting with recurrent attacks of angioedema. The most commonly involved organs include the extremites, face, neck, upper respiratory tract, genital region and the gastrointestinal tract. Edema of the intestinal mucosa can...

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Main Authors: Deniz Özçeker, Zeynep Tamay, Agop Çitak, Muhammet Bulut, Nermin Güler
Format: Article
Language:English
Published: Galenos Yayinevi 2015-03-01
Series:Haseki Tıp Bülteni
Subjects:
Online Access:http://www.hasekidergisi.com/article_8711/A-Rare-Cause-Of-Abdominal-Pain-In-Children-Hereditary-Angioedema
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spelling doaj-9103ea71ee3e4b658782258806f1608c2020-11-25T02:47:52ZengGalenos YayineviHaseki Tıp Bülteni1302-00722147-26882015-03-015319810010.4274/haseki.2064A Rare Cause of Abdominal Pain in Children: Hereditary AngioedemaDeniz Özçeker0Zeynep Tamay1Agop Çitak2Muhammet Bulut3Nermin Güler4İstanbul Üniversitesi İstanbul Tıp Fakültesi, Çocuk Alerji ve İmmünoloji Bilim Dalı, İstanbul, Türkiyeİstanbul Üniversitesi İstanbul Tıp Fakültesi, Çocuk Alerji ve İmmünoloji Bilim Dalı, İstanbul, Türkiyeİstanbul Üniversitesi İstanbul Tıp Fakültesi, Çocuk Yoğun Bakım Bilim Dalı, İstanbul, Türkiyeİstanbul Üniversitesi İstanbul Tıp Fakültesi, Çocuk Sağlığı ve Hastalıkları Anabilim Dalı, İstanbul, Türkiyeİstanbul Üniversitesi İstanbul Tıp Fakültesi, Çocuk Alerji ve İmmünoloji Bilim Dalı, İstanbul, Türkiye Hereditary angioedema (HA) is a rare, autosomal-dominant genetic disorder presenting with recurrent attacks of angioedema. The most commonly involved organs include the extremites, face, neck, upper respiratory tract, genital region and the gastrointestinal tract. Edema of the intestinal mucosa can cause temporary obstruction and severe abdominal pain that can be confused with acute abdomen. Pediatricians and emergency physicians should keep in mind this rare disease in the differential diagnosis of severe abdominal pain.http://www.hasekidergisi.com/article_8711/A-Rare-Cause-Of-Abdominal-Pain-In-Children-Hereditary-AngioedemaChildhereditary angioedemaabdominal pain
collection DOAJ
language English
format Article
sources DOAJ
author Deniz Özçeker
Zeynep Tamay
Agop Çitak
Muhammet Bulut
Nermin Güler
spellingShingle Deniz Özçeker
Zeynep Tamay
Agop Çitak
Muhammet Bulut
Nermin Güler
A Rare Cause of Abdominal Pain in Children: Hereditary Angioedema
Haseki Tıp Bülteni
Child
hereditary angioedema
abdominal pain
author_facet Deniz Özçeker
Zeynep Tamay
Agop Çitak
Muhammet Bulut
Nermin Güler
author_sort Deniz Özçeker
title A Rare Cause of Abdominal Pain in Children: Hereditary Angioedema
title_short A Rare Cause of Abdominal Pain in Children: Hereditary Angioedema
title_full A Rare Cause of Abdominal Pain in Children: Hereditary Angioedema
title_fullStr A Rare Cause of Abdominal Pain in Children: Hereditary Angioedema
title_full_unstemmed A Rare Cause of Abdominal Pain in Children: Hereditary Angioedema
title_sort rare cause of abdominal pain in children: hereditary angioedema
publisher Galenos Yayinevi
series Haseki Tıp Bülteni
issn 1302-0072
2147-2688
publishDate 2015-03-01
description Hereditary angioedema (HA) is a rare, autosomal-dominant genetic disorder presenting with recurrent attacks of angioedema. The most commonly involved organs include the extremites, face, neck, upper respiratory tract, genital region and the gastrointestinal tract. Edema of the intestinal mucosa can cause temporary obstruction and severe abdominal pain that can be confused with acute abdomen. Pediatricians and emergency physicians should keep in mind this rare disease in the differential diagnosis of severe abdominal pain.
topic Child
hereditary angioedema
abdominal pain
url http://www.hasekidergisi.com/article_8711/A-Rare-Cause-Of-Abdominal-Pain-In-Children-Hereditary-Angioedema
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