Pattern of lung function decline in patients with amyotrophic lateral sclerosis: implications for timing of noninvasive ventilation
Background The course of lung function decline in amyotrophic lateral sclerosis (ALS) and the effect of noninvasive positive-pressure ventilation (NIPPV) on that decline are uncertain. We sought to model lung function decline, determine when NIPPV is initiated along that course, and assess its impac...
Main Authors: | Tanmay S. Panchabhai, Eduardo Mireles Cabodevila, Erik P. Pioro, Xiaofeng Wang, Xiaozhen Han, Loutfi S. Aboussouan |
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Format: | Article |
Language: | English |
Published: |
European Respiratory Society
2019-09-01
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Series: | ERJ Open Research |
Online Access: | http://openres.ersjournals.com/content/5/3/00044-2019.full |
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