Dermatofibrosarcoma protuberans: Male breast
Dermatofibrosarcoma protuberans (DFSP) is a rare skin tumor of the dermal layer. Incidence is only about one case per million per year. It is a cutaneous soft tissue sarcoma that rarely metastasizes but it has got a malignant potential in 2% of cases. The challenge with DFSP is that the malignant po...
Main Authors: | , , , |
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Format: | Article |
Language: | English |
Published: |
Wolters Kluwer Medknow Publications
2014-01-01
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Series: | Medical Journal of Dr. D.Y. Patil University |
Subjects: | |
Online Access: | http://www.mjdrdypu.org/article.asp?issn=0975-2870;year=2014;volume=7;issue=1;spage=85;epage=87;aulast=Prabhu |
Summary: | Dermatofibrosarcoma protuberans (DFSP) is a rare skin tumor of the dermal layer. Incidence is only about one case per million per year. It is a cutaneous soft tissue sarcoma that rarely metastasizes but it has got a malignant potential in 2% of cases. The challenge with DFSP is that the malignant potential of this tumor depends on the components histologically and on immunohistochemistry. The second challenge is that these tumors cannot be diagnosed on fine needle aspiration and require a core or incisional biopsy. Only in nodular stage we have to diagnose DFSP. This case presented in a male patient simulating malignancy of breast and fine needle aspiration cytology was inconclusive. The treatment also poses a challenge as not all surgeons are well versed with Moh′s surgery and hence here local wide resection was done. All margins were free. Although chemotherapy forms a part of treatment, it is reserved for large and recurrent tumors. |
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ISSN: | 0975-2870 |