Dermatofibrosarcoma protuberans: Male breast

• Main Authors: Vinod V Prabhu, Aslam Shivani, S H Kulkarni, Vishrabdha R Pawar
• Format: Article
• Language: English
• Published: Wolters Kluwer Medknow Publications 2014-01-01
• Series: Medical Journal of Dr. D.Y. Patil University
• Subjects: CD 34; dermatofibrosarcoma protuberans; skin
• Online Access: http://www.mjdrdypu.org/article.asp?issn=0975-2870;year=2014;volume=7;issue=1;spage=85;epage=87;aulast=Prabhu

Dermatofibrosarcoma protuberans (DFSP) is a rare skin tumor of the dermal layer. Incidence is only about one case per million per year. It is a cutaneous soft tissue sarcoma that rarely metastasizes but it has got a malignant potential in 2% of cases. The challenge with DFSP is that the malignant potential of this tumor depends on the components histologically and on immunohistochemistry. The second challenge is that these tumors cannot be diagnosed on fine needle aspiration and require a core or incisional biopsy. Only in nodular stage we have to diagnose DFSP. This case presented in a male patient simulating malignancy of breast and fine needle aspiration cytology was inconclusive. The treatment also poses a challenge as not all surgeons are well versed with Moh′s surgery and hence here local wide resection was done. All margins were free. Although chemotherapy forms a part of treatment, it is reserved for large and recurrent tumors.