Rosai-Dorfman disease of the paranasal sinuses and orbit

Rosai-Dorfman disease, also known as sinus histiocytosis with massive lymphadenopathy, is a benign indolent disorder, characterized by enlarged lymph nodes filled with histiocytes. Extranodal involvement is uncommon. The disease rarely affects the nose and paranasal sinuses. We report a case that pr...

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Main Authors: Afaq Ahmad Khan, Fouzia Siraj, Devinder Rai, Shyam Aggarwal
Format: Article
Language:English
Published: Elsevier 2011-04-01
Series:Hematology/Oncology and Stem Cell Therapy
Online Access:http://www.sciencedirect.com/science/article/pii/S1658387611500433
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spelling doaj-960834fc19ad4cfe8467951fad3932a22020-11-25T01:01:34ZengElsevierHematology/Oncology and Stem Cell Therapy1658-38762011-04-01429496Rosai-Dorfman disease of the paranasal sinuses and orbitAfaq Ahmad Khan0Fouzia Siraj1Devinder Rai2Shyam Aggarwal3Department of Hematology, Sir Ganga Ram Hospital, New Delhi, India; Afaq Ahmad Khan, MD · Department of Hematology, Sir Ganga Ram Hospital, 3/17 Third Floor, Old Rajinder Nagar, New Delhi, 110060 India · T: +919419003346 F: 25861002Department of Pathology, Sir Ganga Ram Hospital, New Delhi, IndiaDepartment of ENT, Sir Ganga Ram Hospital, New Delhi, IndiaDepartment of Medical Oncology, Sir Ganga Ram Hospital, New Delhi, IndiaRosai-Dorfman disease, also known as sinus histiocytosis with massive lymphadenopathy, is a benign indolent disorder, characterized by enlarged lymph nodes filled with histiocytes. Extranodal involvement is uncommon. The disease rarely affects the nose and paranasal sinuses. We report a case that presented with a right nasal mass, extending into all the paranasal sinuses and right orbit without any accompanying lymphadenopathy. Because of the absence of lymphadenopathy it posed a diagnostic challenge until the pathology was confirmed on histopathological examination.http://www.sciencedirect.com/science/article/pii/S1658387611500433
collection DOAJ
language English
format Article
sources DOAJ
author Afaq Ahmad Khan
Fouzia Siraj
Devinder Rai
Shyam Aggarwal
spellingShingle Afaq Ahmad Khan
Fouzia Siraj
Devinder Rai
Shyam Aggarwal
Rosai-Dorfman disease of the paranasal sinuses and orbit
Hematology/Oncology and Stem Cell Therapy
author_facet Afaq Ahmad Khan
Fouzia Siraj
Devinder Rai
Shyam Aggarwal
author_sort Afaq Ahmad Khan
title Rosai-Dorfman disease of the paranasal sinuses and orbit
title_short Rosai-Dorfman disease of the paranasal sinuses and orbit
title_full Rosai-Dorfman disease of the paranasal sinuses and orbit
title_fullStr Rosai-Dorfman disease of the paranasal sinuses and orbit
title_full_unstemmed Rosai-Dorfman disease of the paranasal sinuses and orbit
title_sort rosai-dorfman disease of the paranasal sinuses and orbit
publisher Elsevier
series Hematology/Oncology and Stem Cell Therapy
issn 1658-3876
publishDate 2011-04-01
description Rosai-Dorfman disease, also known as sinus histiocytosis with massive lymphadenopathy, is a benign indolent disorder, characterized by enlarged lymph nodes filled with histiocytes. Extranodal involvement is uncommon. The disease rarely affects the nose and paranasal sinuses. We report a case that presented with a right nasal mass, extending into all the paranasal sinuses and right orbit without any accompanying lymphadenopathy. Because of the absence of lymphadenopathy it posed a diagnostic challenge until the pathology was confirmed on histopathological examination.
url http://www.sciencedirect.com/science/article/pii/S1658387611500433
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AT devinderrai rosaidorfmandiseaseoftheparanasalsinusesandorbit
AT shyamaggarwal rosaidorfmandiseaseoftheparanasalsinusesandorbit
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