Persistent Left Superior Vena Cava with Absent Right Superior Vena Cava and Discrete Subaortic Stenosis Diagnosed in a Patient with Sick Sinus Syndrome: A Case Report and Brief Review of the Literature
A persistent left superior vena cava (PLSVC) is the most frequent anomaly of the venous drainage system. While both a right and left superior vena cava (SVC) are usually present, a unique, left-sided SVC, also known as an isolated PLSVC, accounts for only 10–20% of cases. It is frequently associated...
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doaj-96e0d26eff9743a3a55894d9e2e32fa82020-11-25T03:57:27ZengMDPI AGDiagnostics2075-44182020-10-011084784710.3390/diagnostics10100847Persistent Left Superior Vena Cava with Absent Right Superior Vena Cava and Discrete Subaortic Stenosis Diagnosed in a Patient with Sick Sinus Syndrome: A Case Report and Brief Review of the LiteratureIrina Demșa0Daniela Crișu1Cristian Mihai Ștefan Haba2Andreea Maria Ursaru3Vlad-Adrian Afrăsânie4Irina Iuliana Costache5Antoniu Octavian Petriș6Dan Nicolae Tesloianu7Department of Cardiology, Emergency Clinical Hospital “Sf. Spiridon”, Bd. Independenței nr. 1, 700111 Iași, RomaniaDepartment of Cardiology, Emergency Clinical Hospital “Sf. Spiridon”, Bd. Independenței nr. 1, 700111 Iași, RomaniaDepartment of Cardiology, Emergency Clinical Hospital “Sf. Spiridon”, Bd. Independenței nr. 1, 700111 Iași, RomaniaDepartment of Cardiology, Emergency Clinical Hospital “Sf. Spiridon”, Bd. Independenței nr. 1, 700111 Iași, RomaniaDepartment of Medical Oncology, “Grigore.T. Popa” University of Medicine and Pharmacy, str. Universitatii nr. 16, 700083 Iași, RomaniaDepartment of Cardiology, Emergency Clinical Hospital “Sf. Spiridon”, Bd. Independenței nr. 1, 700111 Iași, RomaniaDepartment of Cardiology, Emergency Clinical Hospital “Sf. Spiridon”, Bd. Independenței nr. 1, 700111 Iași, RomaniaDepartment of Cardiology, Emergency Clinical Hospital “Sf. Spiridon”, Bd. Independenței nr. 1, 700111 Iași, RomaniaA persistent left superior vena cava (PLSVC) is the most frequent anomaly of the venous drainage system. While both a right and left superior vena cava (SVC) are usually present, a unique, left-sided SVC, also known as an isolated PLSVC, accounts for only 10–20% of cases. It is frequently associated with arrhythmias and other congenital cardiac anomalies. Though it is usually an asymptomatic condition, it may pose significant problems whenever central venous access is needed. We report a case of an isolated PLSVC that was diagnosed incidentally during pacemaker implantation for sinus node dysfunction. The venous anomaly was associated with subvalvular aortic stenosis determined by a subaortic membrane; this particular association of congenital cardiovascular anomalies is a rare finding, with only a few cases reported in the literature. We aim to highlight the clinical and practical implications of this condition, as well as to discuss the embryonic development and diagnostic methods of this congenital defect.https://www.mdpi.com/2075-4418/10/10/847persistent left superior vena cavaabsent right superior vena cavadilated coronary sinuspacemaker implantationdiscrete subaortic stenosis |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Irina Demșa Daniela Crișu Cristian Mihai Ștefan Haba Andreea Maria Ursaru Vlad-Adrian Afrăsânie Irina Iuliana Costache Antoniu Octavian Petriș Dan Nicolae Tesloianu |
spellingShingle |
Irina Demșa Daniela Crișu Cristian Mihai Ștefan Haba Andreea Maria Ursaru Vlad-Adrian Afrăsânie Irina Iuliana Costache Antoniu Octavian Petriș Dan Nicolae Tesloianu Persistent Left Superior Vena Cava with Absent Right Superior Vena Cava and Discrete Subaortic Stenosis Diagnosed in a Patient with Sick Sinus Syndrome: A Case Report and Brief Review of the Literature Diagnostics persistent left superior vena cava absent right superior vena cava dilated coronary sinus pacemaker implantation discrete subaortic stenosis |
author_facet |
Irina Demșa Daniela Crișu Cristian Mihai Ștefan Haba Andreea Maria Ursaru Vlad-Adrian Afrăsânie Irina Iuliana Costache Antoniu Octavian Petriș Dan Nicolae Tesloianu |
author_sort |
Irina Demșa |
title |
Persistent Left Superior Vena Cava with Absent Right Superior Vena Cava and Discrete Subaortic Stenosis Diagnosed in a Patient with Sick Sinus Syndrome: A Case Report and Brief Review of the Literature |
title_short |
Persistent Left Superior Vena Cava with Absent Right Superior Vena Cava and Discrete Subaortic Stenosis Diagnosed in a Patient with Sick Sinus Syndrome: A Case Report and Brief Review of the Literature |
title_full |
Persistent Left Superior Vena Cava with Absent Right Superior Vena Cava and Discrete Subaortic Stenosis Diagnosed in a Patient with Sick Sinus Syndrome: A Case Report and Brief Review of the Literature |
title_fullStr |
Persistent Left Superior Vena Cava with Absent Right Superior Vena Cava and Discrete Subaortic Stenosis Diagnosed in a Patient with Sick Sinus Syndrome: A Case Report and Brief Review of the Literature |
title_full_unstemmed |
Persistent Left Superior Vena Cava with Absent Right Superior Vena Cava and Discrete Subaortic Stenosis Diagnosed in a Patient with Sick Sinus Syndrome: A Case Report and Brief Review of the Literature |
title_sort |
persistent left superior vena cava with absent right superior vena cava and discrete subaortic stenosis diagnosed in a patient with sick sinus syndrome: a case report and brief review of the literature |
publisher |
MDPI AG |
series |
Diagnostics |
issn |
2075-4418 |
publishDate |
2020-10-01 |
description |
A persistent left superior vena cava (PLSVC) is the most frequent anomaly of the venous drainage system. While both a right and left superior vena cava (SVC) are usually present, a unique, left-sided SVC, also known as an isolated PLSVC, accounts for only 10–20% of cases. It is frequently associated with arrhythmias and other congenital cardiac anomalies. Though it is usually an asymptomatic condition, it may pose significant problems whenever central venous access is needed. We report a case of an isolated PLSVC that was diagnosed incidentally during pacemaker implantation for sinus node dysfunction. The venous anomaly was associated with subvalvular aortic stenosis determined by a subaortic membrane; this particular association of congenital cardiovascular anomalies is a rare finding, with only a few cases reported in the literature. We aim to highlight the clinical and practical implications of this condition, as well as to discuss the embryonic development and diagnostic methods of this congenital defect. |
topic |
persistent left superior vena cava absent right superior vena cava dilated coronary sinus pacemaker implantation discrete subaortic stenosis |
url |
https://www.mdpi.com/2075-4418/10/10/847 |
work_keys_str_mv |
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