Pediatric patient with diagnosis of extra osseous Ewing’s sarcoma of the tongue: case report
Ewing’s sarcoma is a malignant tumor that arises mainly from bone tissue, so that its extra-osseous presentation is not very common and even more unusual, in the soft tissues of the oral cavity. The objective of this case was to describe the clinical characteristics of an extra-osseous Ewing’s Sarco...
Main Authors: | , , , , , |
---|---|
Format: | Article |
Language: | English |
Published: |
Faculdade São Leopoldo Mandic
2018-12-01
|
Series: | RGO: Revista Gaúcha de Odontologia |
Subjects: | |
Online Access: | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1981-86372018000400399&lng=pt&nrm=iso&tlng=en |
id |
doaj-9ea592b507884461a265fd36ea545a52 |
---|---|
record_format |
Article |
spelling |
doaj-9ea592b507884461a265fd36ea545a522020-11-25T02:03:41ZengFaculdade São Leopoldo MandicRGO: Revista Gaúcha de Odontologia0103-69711981-86372018-12-01664399403http://dx.doi.org/10.1590/1981-8637201800040000153608Pediatric patient with diagnosis of extra osseous Ewing’s sarcoma of the tongue: case reportNeira CHAPARRO 0Amaurys DIAZ1Luis HERRERA2Rafael PINEDA3Betty PEROZO4Blanca ALVAREZ5Universidad del ZuliaUniversidad del ZuliaUniversidad del ZuliaUniversidad del ZuliaUniversidad del ZuliaHospital Universitario de MaracaiboEwing’s sarcoma is a malignant tumor that arises mainly from bone tissue, so that its extra-osseous presentation is not very common and even more unusual, in the soft tissues of the oral cavity. The objective of this case was to describe the clinical characteristics of an extra-osseous Ewing’s Sarcoma of the tongue in a pediatric patient. An 11-year-old male school patient, who attended an oral medicine consultation referring a volume increase in the tongue. Intraorally, a tumoral lesion was observed on the left lateral edge of the tongue, indurated, with the same color of the mucosa with ulcerated areas, well defined edges and symptomatic on palpation, with an approximate size of 2.5 cm. A cervical and maxillofacial MRI was indicated, observing a partially delimited hyperintense and non-infiltrating lesion in the described area. An incisional biopsy was performed with histopathological diagnosis of malignant neoplasm of blue round cells, theCD99 marker was found to be positive in the immunohistochemical study and was key to the definitive diagnosis of this tumor. A thoraco-abdomino-pelvic tomography was requested by the Pediatric Oncology service, as well as biopsy and aspiration of bone marrow, in which no neoplastic infiltrations were evidenced. After four cycles of chemotherapy, total removal of the lesion was performed with a consecutive histopathological study of the surgical piece, indicating free edges of the lesion. Ewing’s sarcoma is a tumor with aggressive behavior, so this case represents a finding of clinical and epidemiological relevance, both due to its extra-osseous appearance and its unusual behavior.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1981-86372018000400399&lng=pt&nrm=iso&tlng=enEwing’s sarcoma; Mouth; Sarcoma; Tongue |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Neira CHAPARRO Amaurys DIAZ Luis HERRERA Rafael PINEDA Betty PEROZO Blanca ALVAREZ |
spellingShingle |
Neira CHAPARRO Amaurys DIAZ Luis HERRERA Rafael PINEDA Betty PEROZO Blanca ALVAREZ Pediatric patient with diagnosis of extra osseous Ewing’s sarcoma of the tongue: case report RGO: Revista Gaúcha de Odontologia Ewing’s sarcoma; Mouth; Sarcoma; Tongue |
author_facet |
Neira CHAPARRO Amaurys DIAZ Luis HERRERA Rafael PINEDA Betty PEROZO Blanca ALVAREZ |
author_sort |
Neira CHAPARRO |
title |
Pediatric patient with diagnosis of extra osseous Ewing’s sarcoma of the tongue: case report |
title_short |
Pediatric patient with diagnosis of extra osseous Ewing’s sarcoma of the tongue: case report |
title_full |
Pediatric patient with diagnosis of extra osseous Ewing’s sarcoma of the tongue: case report |
title_fullStr |
Pediatric patient with diagnosis of extra osseous Ewing’s sarcoma of the tongue: case report |
title_full_unstemmed |
Pediatric patient with diagnosis of extra osseous Ewing’s sarcoma of the tongue: case report |
title_sort |
pediatric patient with diagnosis of extra osseous ewing’s sarcoma of the tongue: case report |
publisher |
Faculdade São Leopoldo Mandic |
series |
RGO: Revista Gaúcha de Odontologia |
issn |
0103-6971 1981-8637 |
publishDate |
2018-12-01 |
description |
Ewing’s sarcoma is a malignant tumor that arises mainly from bone tissue, so that its extra-osseous presentation is not very common and even more unusual, in the soft tissues of the oral cavity. The objective of this case was to describe the clinical characteristics of an extra-osseous Ewing’s Sarcoma of the tongue in a pediatric patient. An 11-year-old male school patient, who attended an oral medicine consultation referring a volume increase in the tongue. Intraorally, a tumoral lesion was observed on the left lateral edge of the tongue, indurated, with the same color of the mucosa with ulcerated areas, well defined edges and symptomatic on palpation, with an approximate size of 2.5 cm. A cervical and maxillofacial MRI was indicated, observing a partially delimited hyperintense and non-infiltrating lesion in the described area. An incisional biopsy was performed with histopathological diagnosis of malignant neoplasm of blue round cells, theCD99 marker was found to be positive in the immunohistochemical study and was key to the definitive diagnosis of this tumor. A thoraco-abdomino-pelvic tomography was requested by the Pediatric Oncology service, as well as biopsy and aspiration of bone marrow, in which no neoplastic infiltrations were evidenced. After four cycles of chemotherapy, total removal of the lesion was performed with a consecutive histopathological study of the surgical piece, indicating free edges of the lesion. Ewing’s sarcoma is a tumor with aggressive behavior, so this case represents a finding of clinical and epidemiological relevance, both due to its extra-osseous appearance and its unusual behavior. |
topic |
Ewing’s sarcoma; Mouth; Sarcoma; Tongue |
url |
http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1981-86372018000400399&lng=pt&nrm=iso&tlng=en |
work_keys_str_mv |
AT neirachaparro pediatricpatientwithdiagnosisofextraosseousewingssarcomaofthetonguecasereport AT amaurysdiaz pediatricpatientwithdiagnosisofextraosseousewingssarcomaofthetonguecasereport AT luisherrera pediatricpatientwithdiagnosisofextraosseousewingssarcomaofthetonguecasereport AT rafaelpineda pediatricpatientwithdiagnosisofextraosseousewingssarcomaofthetonguecasereport AT bettyperozo pediatricpatientwithdiagnosisofextraosseousewingssarcomaofthetonguecasereport AT blancaalvarez pediatricpatientwithdiagnosisofextraosseousewingssarcomaofthetonguecasereport |
_version_ |
1724946457221398528 |